Primary pulmonary rhabdomyosarcoma is a rare lesion, especially in pediatric patients. Of the 22 described patients with primary pulmonary rhabdomyosarcoma, only two were less than 20 years of age.1-17 In this article, we describe a child with primary pulmonary rhabdomyosarcoma in whom treatment by surgical excision and chemotherapy resulted in five-year disease-free survival.Report of a Case.\p=m-\A 21-month-old boy