Primary retroperitoneal mucinous cystadenoma of borderline malignancy in a male patient. Case report and review of the literature

Abstract

BackgroundPrimary retroperitoneal mucinous cystadenoma of borderline malignancy represents a rare tumor, with unclear histogenesis, concerning almost exclusively women. Only two cases concerning male patients have been reported.Case reportWe herein report a case of a 37 year old man undergone laparotomy for a sizable retroperitoneal tumor resulting after the histological examination to a primary retroperitoneal mucinous cystadenoma of borderline malignancy.ConclusionThis is the third case of primary retroperitoneal mucinous cystadenoma of borderline malignancy in a male patient reported in the literature. The preoperative diagnosis is impossible. Laparotomy constitutes the only diagnostic and curative approach.

Retropancreatic Ovarian Tumor

“…This is the same profile encountered in ovarian mucinous tumors. However, the cases reported so far have not shown any germ cell (ovarian follicle) derivatives [7,8]. The fact that this tumor is also occasionally found in men and ovarian follicle (germ cell derivative) has not been detected previously has made the Bectopic ovary^theory weak [7].…”

“…A meticulous sampling of the resected tumor is necessary to search for rare occurrence of borderline malignancy or a carcinomatous focus [2]. In women with focus of carcinoma, some authors suggest ovariectomy or hysterectomy [7].…”

A rare case of a primary retroperitoneal mucinous cystic tumour with borderline malignancy and literature review

“…To date, only 26 confirmed cases of PRMCN with borderline malignancy have been reported (table 1). 1 4 8–24 Data analysis suggests that this tumour is more frequent in women with a wide age range from 22 to 68 years (median age 40.3 years) and very rare in man with just five cases described 1 10 21 22 24…”

“…Primary retroperitoneal tumours are uncommon neoplasms, corresponding to 0.01%–0.2% of all neoplasias 1. Some of them may have a mucinous cystic type, being extremely rare with only 144 cases described in the literature 2…”

Primary retroperitoneal mucinos cystadenoma: A case report

“…Međutim, to se izbegava zbog rizika od ponovne pojave i diseminacije kod cističnih tumora. aspiracija cističnog tumora nije dovoljna za otkrivanje ćelija zida ovog cističnog tumora (25). jedini način lečenja i postavljanja definitivne dijagnoze jeste totalna ekstirpacija i patohiostološka verifikacija ciste, što je učinjeno kod opisanog bolesnika.…”