Primary Renal Rhabdomyosarcoma: An Unusual Bone Metastasizing Tumor of Kidney

Parvin, Shabnam; Ghosh, Ranajoy; Das, Ram; Saha, Koushik; Roy, Paromita; Datta, Chhanda; Chatterjee, Uttara

doi:10.1080/15513815.2016.1175528

Cited by 9 publications

(5 citation statements)

References 20 publications

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“…About 5%‐10% of tumors radiologically diagnosed as Wilms' tumor may prove to be benign. These benign lesions can be congenital mesoblastic nephroma, cellular congenital mesoblastic nephroma, cystic partially differentiated nephroblastoma and even tubercular pyelonephritis …”

Section: Discussionmentioning

confidence: 99%

“…About 5%-10% of tumors radiologically diagnosed as Wilms' tumor may prove to be benign. These benign lesions can be congenital mesoblastic nephroma, cellular congenital mesoblastic nephroma, cystic partially differentiated nephroblastoma and even tubercular pyelonephritis 10. FNAC is an important as diagnostic tool for accurate diagnosis of pediatric renal tumours and selection of appropriate chemotherapy.Interpretation of aspirationsmears of CCSK is difficult because of presence of varying proportion of three cell types-cord cells, septal cells and small pyknotic cells.…”

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confidence: 99%

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FNAC aided diagnosis of clear cell sarcoma of kidney: Report of two cases in infants

Das

Dalal³

et al. 2017

Diagnostic Cytopathology

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Clear cell sarcoma of kidney (CCSK) is a rare aggressive malignant renal neoplasm with a high metastatic potential. Its outcome has however, improved with the advent of doxorubicin based neoadjuvant chemotherapy. Here, we present two cases of CCSK in infants diagnosed on cytology followed by nephrectomy. The first case presented in the neonatal period and had the unusual histological finding of islands of cartilage. The second case presented at the age of eight months. The possibility of CCSK should, therefore, be considered in the differential diagnoses of renal masses in infants as well as neonates. Diagn. Cytopathol. 2017;45:761-765. © 2017 Wiley Periodicals, Inc.

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Section: Discussionmentioning

confidence: 99%

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confidence: 99%

FNAC aided diagnosis of clear cell sarcoma of kidney: Report of two cases in infants

Das

Dalal³

et al. 2017

Diagnostic Cytopathology

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“…This approach, tailored for pediatric patients, has also been widely adopted in the management of adult RMS. The implementation of multimodality treatment has significantly improved survival outcomes, with reported cure rates ranging from 70% to 90% in pediatric RMS cases [7][8][9].…”

Section: Discussionmentioning

confidence: 99%

A Rare Case of Rhabdosarcoma on the Upper Pole of the Kidney

Ashrita,

Naik,

Ethuri

et al. 2024

Cureus

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Rhabdomyosarcoma arising from the upper pole of the kidney is an exceedingly rare occurrence, with only a few documented cases reported in the literature. Here, we present a case of a one-year-old Indian male child diagnosed with rhabdomyosarcoma localized to the upper pole of the kidney. The patient presented with abdominal distension persisting for three days, and imaging studies revealed a mass consistent with renal sarcoma. Surgical excision was performed, followed by histopathological examination confirming the diagnosis of rhabdomyosarcoma. Despite aggressive management, the patient's prognosis remains guarded due to the disease's aggressive nature. This case highlights the importance of considering rhabdomyosarcoma in the differential diagnosis of renal masses, particularly in atypical locations. Early diagnosis and a multimodal treatment approach are crucial for optimizing outcomes in such rare cases.

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“…There are rare reports of other primary renal SRBCTs, including desmoplastic small round cell tumor and primary renal lymphoma. [15][16][17][18] While primary renal ESFTs are rare, this etiology must be considered in the differential for a primary renal tumor, to prevent incorrect diagnoses with misdirected treatment.…”

Section: Discussionmentioning

confidence: 99%

Primary Renal Ewing Sarcoma in Children and Young Adults

Bradford

Nobori²,

Johnson³

et al. 2020

Journal of Pediatric Hematology/Oncology

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The Ewing sarcoma family of tumors (ESFT) are high-grade small round blue cell malignancies traditionally presenting in children and adolescents. The most common site of primary disease is bone, though extraskeletal primary sites are well-recognized. 1 We present six cases of primary ESFT of the kidney and one case of the adrenal gland. Patients were 11-18 years of age at diagnosis. Metastases at diagnosis were present in most cases (n=6). All patients underwent surgery, and most received radiation (n=5). Five patients relapsed after initial remission.Comprehensive review of the primary renal ESFT literature was used to analyze various factors, including age, gender, disease metrics, metastases at diagnoses, and overall survival in a total of 362 cases. Notably, while the general ESFT population has reported rates of metastasis at diagnosis of 20-25%, 2 this rate in the renal ESFT population was 53% with a rate of 59% in adolescent and young-adult (AYA) patients (11-24 years). Nodal disease at diagnosis was present in 24% of renal ESFT cases compared with 3.2% in patients with primary skeletal ESFT. 3 While this malignant process may share histologic and molecular features with its bone and soft tissue counterparts, primary renal ESFT presentations appear to be more aggressive and have worse outcomes.

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Primary Renal Rhabdomyosarcoma: An Unusual Bone Metastasizing Tumor of Kidney

Cited by 9 publications

References 20 publications

FNAC aided diagnosis of clear cell sarcoma of kidney: Report of two cases in infants

FNAC aided diagnosis of clear cell sarcoma of kidney: Report of two cases in infants

A Rare Case of Rhabdosarcoma on the Upper Pole of the Kidney

Primary Renal Ewing Sarcoma in Children and Young Adults

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