Primary pulmonary artery Rosai-Dorfman disease mimicking sarcoma

Morsolini, Marco; Nicola, Marta Di; Paulli, Marco; D’Armini, Andrea Maria

doi:10.1016/j.jtcvs.2013.08.001

Cited by 4 publications

(1 citation statement)

References 4 publications

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“…39 RDD may also affect the cardiac valves or pericardium. 32 Involvement of the heart and great vessels may mimic a neoplastic process such as a sarcoma on CT or MR. 40 Nodal RDD is usually a self-limiting disease. Chemotherapy agents used in lymphoma as well as steroids are available treatment options.…”

Section: Pulmonary Langerhans Cell Histiocytosismentioning

confidence: 99%

Cardiothoracic manifestations of primary histiocytoses

Vargas¹,

Richards²,

Ocazionez³

et al. 2016

The British Journal of Radiology

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The objectives of this article were: (1) to review common and rare manifestations of systemic and pulmonary Langerhans cell histiocytosis, Rosai-Dorfman disease, Erdheim-Chester disease and juvenile xanthogranuloma; (2) to provide the reader with important pathologic, epidemiologic and clinical features of these diseases. The histiocytoses are a diverse group of diseases which typically manifest with multiorgan involvement. Understanding the pathologic, epidemiologic and clinical features of these entities can help the radiologist suggest an accurate diagnosis of histiocytosis when typical imaging features are encountered.

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Section: Pulmonary Langerhans Cell Histiocytosismentioning

confidence: 99%

Cardiothoracic manifestations of primary histiocytoses

Vargas¹,

Richards²,

Ocazionez³

et al. 2016

The British Journal of Radiology

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Heart failure with multiple cardiac masses: Extensive cardiac involvement in Rosai–Dorfman disease

Ghosh

Rebecca

Joseph

et al. 2018

IHJ Cardiovascular Case Reports (CVCR)

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Extranodal Rosai–Dorfman Disease Presenting as a Mediastinal Mass with Pulmonary Artery Invasion

Orr

Lefler

Deshpande

et al. 2018

Case Reports in Hematology

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Rosai–Dorfman disease (RDD) is a rare, nonmalignant disorder of histiocyte proliferation typically involving the cervical lymph nodes. However, a subset of patients with RDD will display extranodal manifestations that are highly variable in presentation, more challenging to diagnose, and less likely to spontaneously regress compared to nodal disease. While case reports of extranodal involvement in nearly every organ system exist, documented instances of mediastinal and pulmonary artery involvement are particularly rare. This study describes the case of a middle-aged woman presenting with new onset right heart failure who was found to have extranodal RDD in the form of a large mediastinal mass with invasion and occlusion of the main pulmonary arteries.

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Primary pulmonary artery Rosai-Dorfman disease mimicking sarcoma

Cited by 4 publications

References 4 publications

Cardiothoracic manifestations of primary histiocytoses

Cardiothoracic manifestations of primary histiocytoses

Heart failure with multiple cardiac masses: Extensive cardiac involvement in Rosai–Dorfman disease

Extranodal Rosai–Dorfman Disease Presenting as a Mediastinal Mass with Pulmonary Artery Invasion

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