Primary primitive neuroectodermal tumour arising in the small bowel

Sethi, B; Smith, Graeme D

doi:10.1111/j.1365-2559.2007.02631.x

Cited by 18 publications

(7 citation statements)

References 6 publications

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“…The clinical symtomatology is poor, dominated by locoregional signs related to the mass syndrome (pain, palpable mass) [8] [19] [22] [31] [32] [36]. Complications such as occlusion, perforation or rupture may occur [15] [16] [21] [24] [25] [28] [38]. Ileal PNET may be revealed by metastasis in advanced stages of the disease [30].…”

Section: Discussionmentioning

confidence: 99%

Peripheral Primary Neuroectodermal Tumour of the Ileum: A Case Report and Review of the Literature

Soukaina¹,

Lemsanes²,

Razine³

et al. 2021

JCT

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Background: Ewing's Sarcoma (ES)/peripheral Primitive Neuroectodermal Tumor (pPNET) is a rare aggressive malignant small round cell tumour. Most of them arise in bony sites, and they represent the second commonest primary osseous malignancy in adolescence and young adults. The localization of the small bowel is very rare, to our knowledge only 35 cases of ES/pPNET of the small bowel have been reported in the literature. Case Presentation: We report a case of pPNET of the ileum in a 26-year-old female, presented abdominal pain with a transit disorder. The clinical examination was unremarkable. The histological and immunohistochemical study confirmed the diagnosis of peripheral primary neuroectodermal tumours. The patient was treated by tumor resection followed by adjuvant chemotherapy. The evolution was good, without recurrence with a follow-up of 12 months. Conclusion: PNET of the ileum is very rare. We report this case to enrich the database of this rare clinical entity and to improve the management of patients with PNET of the ileum.

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Section: Discussionmentioning

confidence: 99%

Peripheral Primary Neuroectodermal Tumour of the Ileum: A Case Report and Review of the Literature

Soukaina¹,

Lemsanes²,

Razine³

et al. 2021

JCT

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“…There have been a number of case reports for peripheral PNETs including those in the eye [ 2 , 3 ], maxillo-facial [ 4 - 6 ], peripheral limbs [ 7 , 8 ], gynaecological organs [ 9 - 11 ] and intraabdominal [ 12 , 13 ]. There have been reports of skin and subcutaneous PNETs mainly in children, adolescents and young adults [ 14 ] and very few reports specifically regarding abdominal subcutaneous PNET and the only ones have been in children [ 15 , 16 ].…”

Section: Discussionmentioning

confidence: 99%

Primitive Neuroectodermal Tumour (PNET) in subcutaneous abdominal wall: a case report

Betal

Shaygi

Babu

et al. 2009

Int Semin Surg Oncol

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Primitive neuroectodermal tumour (PNET) is a rare tumour mainly found in children under ten years old. It may be broadly categorised into those occurring from the central or peripheral nervous system of which the majority arise centrally. We report a 61 year-old lady who had previous lobular breast cancer presenting with a rapidly expanding lesion in her anterior right upper abdominal wall. Clinically it appeared to be benign, however, histopathology of the excised lesion revealed a localised PNET. This case is an unusual case of a PNET in an adult that is peripheral in nature arising from subcutaneous tissue in the abdominal wall.

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“…Although Ewing's sarcomas are more common in the bone there are examples of extra osseous tumours that may resemble PNET. There have been a number of case reports for peripheral PNETs including those in the eye [6,7], gynaecological organs [8,9,10] and intraabdominal sites [11,12], kidneys [13,14], skin and subcutaneous tissue [15]. Among all these sites intraabdominal site is very rare.…”

Section: Discussionmentioning

confidence: 99%