Primary pleomorphic rhabdomyosarcoma of the kidney in an adult

Dalfior, Daniela; Eccher, Albino; Gobbo, Stefano; Brunelli, Matteo; Martignoni, Guido; Menestrina, Fabio; Dalla, Palma Paolo; Dvornik, G.

doi:10.1016/j.anndiagpath.2007.01.005

Cited by 14 publications

(10 citation statements)

References 8 publications

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“… 22 , 23 Additional stains are obtained to differentiate RMS from other malignancies, for example, rhabdoid tumors, sarcomatoid RCC, angiomyolipoma, and Wilm's tumor. 24 – 26 …”

Section: Discussionmentioning

confidence: 99%

Primary Renal Rhabdomyosarcoma in an Adolescent With Tumor Thrombosis in the Inferior Vena Cava and Right Atrium

et al. 2016

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Although the second peak of the age distribution of rhabdomyosarcoma (RMS) is at adolescence, renal RMS is extremely rare at this age group. This tumor is indistinguishable from other renal tumors based on clinical and imaging findings, and the diagnosis relies on histology and immunohistochemical staining. We report a unique case of adolescent renal RMS associated with tumor thrombus extending into the inferior vena cava (IVC) and right atrium.An 18-year-old female adolescent presented with shortness of breath and palpitations, associated with right flank discomfort, and hematuria. A pleomorphic-type renal RMS with Budd–Chiari syndrome and arrhythmia induced by IVC and RA thrombosis was diagnosed. Despite complete tumor resection, the patient developed multiple lung metastases a month after surgery. Chemotherapy was recommended, but the patient declined. She died within a year of the initial operation.Adolescent renal RMS is rare and associated with poor outcome. Early aggressive multimodal therapy seems to be appropriate, in particular, in the presence of tumor thrombosis.

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“… 22 , 23 Additional stains are obtained to differentiate RMS from other malignancies, for example, rhabdoid tumors, sarcomatoid RCC, angiomyolipoma, and Wilm's tumor. 24 – 26 …”

Section: Discussionmentioning

confidence: 99%

Primary Renal Rhabdomyosarcoma in an Adolescent With Tumor Thrombosis in the Inferior Vena Cava and Right Atrium

et al. 2016

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“…RMS may occur in all age groups but is more prevalent in the first and second decades of life, with a peak between 2 and 6 years of age [7], representing approximately 4–8% of all pediatric cancers [8]. Although head and neck tumors are rare in children [9], approximately 60% of all pediatric RMS cases occur in the head and neck [9, 10, 11]. …”

Section: Discussionmentioning

confidence: 99%

Orbito-Ethmoidal Rhabdomyosarcoma in an Adult Patient: A Case Report and Review of the Literature

Sepúlveda

Spencer²,

Cabezas

et al. 2014

Case Rep Oncol

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We report a patient who presented to the ENT service complaining of nasal obstruction, exophthalmos, edema and ipsilateral facial congestion. Imaging studies revealed an aggressive noncalcified solid mass centered in the left nasoethmoidal region and heterogeneous avid enhancement following contrast media injection. Subsequently, a biopsy confirmed the presence of solid alveolar rhabdomyosarcoma. The patient was treated with chemoradiation therapy for 7 weeks. Due to the advanced stage of the disease, the patient was enrolled in a palliative care and pain control program.

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“…Of these, rhabdomyosarcomas are the least frequently reported in the literature. Adult cases are uncommon, arise mainly in large skeletal muscles, and are usually of pleomorphic subtype [3]. …”

Section: Discussionmentioning

confidence: 99%

Primary Renal Embryonal Rhabdomyosarcoma in Adults: A Case Report and Review of the Literature

Fanous

Mayer

Vale

et al. 2012

Case Reports in Oncological Medicine

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Primary pleomorphic rhabdomyosarcoma of the kidney in an adult

Cited by 14 publications

References 8 publications

Primary Renal Rhabdomyosarcoma in an Adolescent With Tumor Thrombosis in the Inferior Vena Cava and Right Atrium

Primary Renal Rhabdomyosarcoma in an Adolescent With Tumor Thrombosis in the Inferior Vena Cava and Right Atrium

Orbito-Ethmoidal Rhabdomyosarcoma in an Adult Patient: A Case Report and Review of the Literature

Primary Renal Embryonal Rhabdomyosarcoma in Adults: A Case Report and Review of the Literature

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