“…In the reviewed cases, ten patients underwent surgery with no evidence of improvement in survival [3,6,9,15,19,23,27,35,38,39]. Prompt anthracycline-based chemotherapy has been administrated in 51% of the reviewed cases [1,3,6,7,8,9,12,17,19,20,25,26,29,30,31,38,39,41], resulting in 61% of complete remission (mean follow-up times 17 months; range 3-40 months). Radiotherapy was delivered to 17% of patients, alone or combined with chemotherapy, with a further improvement in survival [3,17,25,26,34,38].…”