“…The most important role of CoQ10 is as an electron carrier, which can shuttle electrons derived from complexes I (NADH: ubiquinone oxidoreductase) and II (succinate dehydrogenase) to complex III (ubiquinone‐cytochrome c oxidoreductase). It is also reported to be involved in several other essential biological processes, such as biosynthesis of pyrimidine, antioxidant response, regulation of the mitochondrial structural stabilization, β‐oxidation of fatty acids, apoptosis, and so on 8 . So far, there are more than 10 genes directly related to biosynthesis of CoQ10 ( ADCK3 , PDSS1 , PDSS2 , COQ2 , COQ3 , COQ4 , COQ5 , COQ6 , COQ7 , COQ8A , COQ8B , COQ9 , COQ10A , and COQ10B ).…”