Primary Antiphospholipid Syndrome Presenting as Budd-Chiari Syndrome

Uncommon presentations of primary systemic necrotizing vasculitides: the Great Masquerades

“…Pomeroy et al ., in 1984, first described this association. Subsequently, there have been multiple case reports of the same . In 2001, Espinosa et al ., reported the largest series to date, comprising of 43 cases of Budd–Chiari syndrome secondary to antiphospholipid syndrome syndrome.…”

“…Subsequently, there have been multiple case reports of the same. [70][71][72][73][74][75][76][77][78][79] In 2001, Espinosa et al, reported the largest series to date, comprising of 43 cases of Budd-Chiari syndrome secondary to antiphospholipid syndrome syndrome. These patients were predominantly females (67%), the majority had primary antiphospholipid syndrome syndrome (74%) and many of them had Budd-Chiari syndrome at presentation (65%).…”