Preduodenal portal vein in association with midgut malrotation and duodenal web—triple anomaly?

Preduodenal portal vein, malrotation, and high jejunal atresia: a case report

“…Being an early embryonic vascular event, it is not surprising that PDPV is very seldom an isolated defect. In most reported cases, it either was a part of the heterotaxia syndrome or polysplenia syndrome or was associated with other congenital anomalies including situs inversus, malrotation, biliary atresia, duodenal atresia, annular pancreas, or cardiac defects [3,4]. In the present report, we describe a case of a newborn affected by PDPV associated with malrotation, a complex cardiac defect, and high jejunal atresia.…”

“…Many authors, however, attribute the duodenal obstruction directly to the PDPV in only a few patients. In most of the cases, duodenal obstruction seems to result from other associated abnormalities as malrotation with Ladd bands, annular pancreas, or intrinsic duodenal membranes [3,4,8]. Reviewing the literature dealing with this subject, we have not found a case of PDPV associated with intestinal atresia.…”

Duodenal obstruction due to a preduodenal portal vein

“…In PDPV, the portal vein passes anterior to the duodenum rather than posterior to it. [1][2][3][4][5][6][7][8] It is generally asymptomatic, but may co-exist with situs inversus and other anomalies like midgut malrotation, duodenal web, pancreatic, splenic or cardiac anomalies. [1][2][3][4][5][6]8] PDPV was first described in 1921 by Knight, and the majority of the reported cases in the literature are children presenting with duodenal obstruction.…”

“…[1][2][3][4][5][6][7][8] It is generally asymptomatic, but may co-exist with situs inversus and other anomalies like midgut malrotation, duodenal web, pancreatic, splenic or cardiac anomalies. [1][2][3][4][5][6]8] PDPV was first described in 1921 by Knight, and the majority of the reported cases in the literature are children presenting with duodenal obstruction. [1][2][3][4][5][6][7][8] The portal vein arises during foetal life by a systematic absorption of the interconnecting veins of the vitelline venous system.…”

“…[1][2][3][4][5][6]8] PDPV was first described in 1921 by Knight, and the majority of the reported cases in the literature are children presenting with duodenal obstruction. [1][2][3][4][5][6][7][8] The portal vein arises during foetal life by a systematic absorption of the interconnecting veins of the vitelline venous system. The two parallel vitelline veins are joined by three interconnecting veins-the cephalad branch within the liver, the middle branch posterior to duodenum, and the caudal branch anterior to duodenum.…”