Pre-Sézary syndrome

Winkelmann, R. K.; Buechner, S. A.; Díaz‐Pérez, J.L.

doi:10.1016/s0190-9622(84)80321-7

Cited by 66 publications

(33 citation statements)

References 13 publications

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“…The laboratory findings are usually normal except for an increased serum IgE level in approximately 70% [ 1], In spite of the term pre-Sezary syndrome coined by Winkelman et al [2], we have not found our patients to develop a true Sezary syndrome. However, 34% developed a cutaneous T-cell lymphoma or were suspected of having mycosis fungoides [ 1 ].…”

contrasting

confidence: 57%

Photopheresis in the Red Man or Pre-Sézary Syndrome

et al. 1995

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Background: The beneficial effect of extracorporeal photochemotherapy has clearly been established for patients with cutaneous T-cell lymphoma with Sézary’s syndrome. But this treatment has not been used in the red man syndrome or pre-Sézary syndrome. Some of these patients do not respond sufficiently or do not tolerate other therapies. Objective: The purpose of this open study was to evaluate the clinical efficacy of photopheresis in this group of patients. Methods: Seven patients with the red man syndrome were treated on 2 consecutive days every 4 weeks for 6–22 months. Six had been on systemic steroids and 3 had also received retinoids without sufficient effects. All were initially treated with topical nitrogen mustard but no longer tolerated this treatment. Results: All signs of erythroderma disappeared in 6 of the 7 patients. All systemic therapy could be discontinued in all but 2 patients. No side effects were observed. Conclusion: Photopheresis may be an effective alternative treatment for this group of patients, when other types of therapy have failed.

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contrasting

confidence: 57%

Photopheresis in the Red Man or Pre-Sézary Syndrome

et al. 1995

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“…It has been reported that non‐diagnostic erythrodermic dermatitis may precede the overt clinical picture of SS 1 . In some patients, the diagnosis of PSES can be made, 2 but this phase was not seen in the patient presented here. A study from our department on 28 patients with an idiopathic erythroderma indicated that only two (7%), including the patient presented here, showed progression of their erythroderma into CTCL 7 …”

Section: Discussionmentioning

confidence: 69%

“…The term pre‐Sézary erythroderma syndrome (PSES) was introduced to describe a non‐diagnostic dermatitis preceding the overt clinical picture of SS, defined by the combination of chronic erythroderma and less than 10% SCs in the peripheral blood. Patients with PSES may have a history of atopic dermatitis (AD) and/or an atopic background 2 …”

mentioning

confidence: 99%

Sézary syndrome in a young man with severe atopic dermatitis

Haselen¹,

Toonstra²,

Preesman³

et al. 1999

British Journal of Dermatology

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Sézary syndrome (SS) is a rare cutaneous T-cell lymphoma. SS usually develops de novo. We describe a 23-year-old man with a proven history of severe atopic dermatitis since childhood, who developed SS. This case contributes to the discussion about the possibility of a relationship between inflammatory dermatitis, atopy and subsequent SS. We provide criteria that should be fulfilled to define such an association.

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“…with erythroderma lasting > 1 month, palmar–plantar keratoderma, and nonspecific histology) could be classified as having a pre‐Sezary syndrome. 28 Such patients should therefore be followed up with a high index of suspicion. Due to the high prevalence of atopic eczema in our sample (23.9%), and the fact that a large number of our patients used herbal medication (17.7%), we agree with Botelia‐Estrada et al .…”

Section: Discussionmentioning

confidence: 99%