Potts shunt in child with suprasystemic pulmonary arterial hypertension

Żuk, Małgorzata; Mazurkiewicz-Antoń, Katarzyna; Mirecka-Rola, Alicja; Kawalec, Wanda

doi:10.5603/kp.2015.0046

Cited by 2 publications

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“…[50][51][52] Since the original description by Blanc and coworkers 49 of successful application of this surgical procedure in 2 boys with suprasystemic PH after an arterial switch for transposition of the great arteries (Figure 2), experience and interest have rapidly expanded. [50][51][52][53][54][55][56][57] The surgical procedure is performed under general anesthesia, usually via a left thoracotomy without cardiopulmonary bypass, and the size of the shunt (which remains controversial) is set at ϳ9 mm.…”

Section: Potts Shuntmentioning

confidence: 99%

“…This procedure often results in significant improvement in functional class, exercise tolerance, and reduced levels of natriuretic peptides in survivors. [49][50][51][52][53][54][55][56][57] However, there is also an inherent risk of mortality during or after this surgical procedure in this very sick PAH population. Also, adults with PAH and severe RVF undergoing this intervention might have a different postoperative prognosis and higher perioperative mortality.…”

Section: Potts Shuntmentioning

confidence: 99%

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Balloon Dilation Atrial Septostomy and Potts Anastomosis for Severe Pulmonary Arterial Hypertension: Why, When, and How

Sandoval

Pulido

Sandoval

et al. 2016

Advances in Pulmonary Hypertension

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Despite advances in pharmacologic treatment, pulmonary arterial hypertension (PAH) remains a fatal disease. In recent years, surgical/interventional approaches including balloon dilation atrial septostomy and Potts anastomosis have been applied to improve the hemodynamic variables associated with right ventricular failure in the setting of PAH. These interventions may improve quality of life and prolong survival in this population. In this review, we will discuss the role of these 2 therapeutic alternatives in the management of PAH.

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Section: Potts Shuntmentioning

confidence: 99%

Section: Potts Shuntmentioning

confidence: 99%

Balloon Dilation Atrial Septostomy and Potts Anastomosis for Severe Pulmonary Arterial Hypertension: Why, When, and How

Sandoval

Pulido

Sandoval

et al. 2016

Advances in Pulmonary Hypertension

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“…In the years 2009-2013 the target-oriented therapy in accordance with current standards (2009) was applied, but with no possibility of treatment with prostacyclin or its analogues in outpatient care. Additionally, lung transplant in young children is virtually inaccessible, and the Potts anastomosis was performed for the first time in 2012 [4]. The survival analysis, depending on treatment, was performed for patients taking advanced therapy (limited as above) immediately after the diagnosis or at any time during the course of the disease, as compared with patients who had never been treated with advanced therapy.…”

Section: Methodsmentioning

confidence: 99%

Prognosis in children with pulmonary arterial hypertension: 10-year single-centre experience

et al. 2016

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A b s t r a c tBackground: Pulmonary arterial hypertension (PAH) is a rare progressive disease of the pulmonary arterioles with an unfavourable prognosis. Aim:To evaluate survival and prognostic factors in patients with PAH diagnosed and treated at a single centre in the years 2004-2013. Methods:The study included 55 children (33 girls; 66%, 22 boys; 33%), with an average age 6.2 ± 6.0 years, with idiopathic PAH -n = 23 (42%), PAH associated with systemic-to-pulmonary shunts -n = 17 (31%), and PAH after corrective cardiac surgery -n = 15 (27%). Forty-seven of them (87%) were treated with advanced therapy.Results: During the follow-up with an average time of 5.6 ± 4.7 years 15 (27.3%) children died. The one-, three-, five-, and ten-year survival was, respectively, 83.1%, 77.1%, 70.7%, and 65.2%. The analysis of the survival curves revealed a better prognosis in patients with baseline N-terminal pro-B-type natriuretic peptide (NT-proBNP) level < 605 pg/mL (p = 0.024) and a higher probability of survival of three and five years in children at baseline I/II World Health Organisation functional class (WHO-FC). The higher risk of death was associated with a higher pressure in the right atrium (HR 1.23, p < 0.01) and higher pulmonary resistance (HR 1.1, p < 0.01), whereas no history of syncope had a better prognosis (HR 0.31, p = 0.03).Conclusions: Survival in the study group was comparable to the currently published register data. Mortality risk factors were connected with the severity of the disease at diagnosis.

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Potts shunt in child with suprasystemic pulmonary arterial hypertension

Cited by 2 publications

References 0 publications

Balloon Dilation Atrial Septostomy and Potts Anastomosis for Severe Pulmonary Arterial Hypertension: Why, When, and How

Balloon Dilation Atrial Septostomy and Potts Anastomosis for Severe Pulmonary Arterial Hypertension: Why, When, and How

Prognosis in children with pulmonary arterial hypertension: 10-year single-centre experience

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