“…Six of the described cases were in children [2][3][4][5]8,10] , and the oldest patient identified was 38 years old at the time of diagnosis [7] . A small gender difference is evident, as the lesions were more often described in women [5,6,9,10] . Clinical manifestations were variable, including jaundice [2,4,10] , portal hypertension [3,6] and a palpable abdominal mass [7,8,10] .…”