Polymorphous hemangioendothelioma of the neck

Recurrent polymorphous haemangioendothelioma

“…Thus, PH should not be classed solely as a peripheral lymph node tumour. Clinical presentation may range from an incidental finding at routine radiological examination to complications due to compression of related structures; enlarged lymph nodes are the most common clinical presentation 1–5 …”

Polymorphous hemangioendothelioma in a child with acquired immunodeficiency syndrome (AIDS)

“…In the first series of patients 1, a 30 year old developed metastatic disease to the lung and died from these metastases 1,2. In another patient, an inguinal relapse occurred 7 years after the initial diagnosis 5. All other patients attained long term cure without adjuvant therapy.…”

“…An additional case report in 2001, presented a 55‐year‐old woman with an intradural, extramedullary nodule 4. Another case report in 2003, presented a woman with previous history of radiation therapy and an intranodal neck lesion 5. A final case report in 2004 presented a 43‐year‐old woman diagnosed in 1997 with a retroperitoneal mass in 1997 and a recurrence in an inguinal node in 2004 6.…”

“…Polymorphous hemangioendothelioma (PH) is a rare vascular tumor, previously only described in the adult population. We have identified only nine cases reported in six prior publications 1–6. It is described as a rare vascular tumor with borderline malignant potential, so named due to its intermediate behavior between hemangiomata and angiosarcoma 5.…”

“…We have identified only nine cases reported in six prior publications 1–6. It is described as a rare vascular tumor with borderline malignant potential, so named due to its intermediate behavior between hemangiomata and angiosarcoma 5. It appears to be most often described as having an association with lymph nodes and presenting as a lymphadenopathy.…”