Poland's syndrome: A case report with review of literature regarding management

Dolas, Shilpy Chauhan; Poovamma, C.U.; Prema, M.; Khandelwal, Rohan; Pais, Anthony Vijay; Kaul, Ashok

doi:10.3233/bd-130361

Cited by 9 publications

(10 citation statements)

References 8 publications

(10 reference statements)

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“…As the most popular perforator flap for postmastectomy breast reconstruction, the DIEP flap is recommended for treating Poland syndrome also because of its ample volume and significantly longer pedicles which allow for more freedom in tissue-tailoring and flap insetting. SGAP [22] and ALT [24, 25] flaps served as alternatives in cases of inadequate abdominal tissue or previous scars. Gautam et al [14]reported the largest series of revision surgeries using perforator flaps for previous implant or flap failure that achieved satisfying long-time results, despite the greater occurrence of short-term complications than with primary reconstructions including hematoma, seroma, and fat necrosis.…”

Section: Discussionmentioning

confidence: 99%

Breast Reconstruction with Perforator Flaps in Poland Syndrome: Report of a Two-Stage Strategy and Literature Review

Liu

2019

Breast Care

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• The latissimus dorsi muscle with implants is routinely used for Poland syndrome breast reconstruction but can yield unsatisfying results due to implant-related complications. • Perforator flaps have mainly been used in revision surgery due to severe implant-related complications but are seldom discussed in the context of primary breast reconstruction in Poland syndrome. Novel Insights • Perforator flaps provide a reliable alternative for breast and chest-wall reconstruction in Poland syndrome. • A 2-stage approach consisting of tissue expansion and deep inferior epigastric perforator flap transfer, successively, attained esthetic restoration of the breast, with satisfying breast symmetry and an inconspicuous scar.

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Section: Discussionmentioning

confidence: 99%

Breast Reconstruction with Perforator Flaps in Poland Syndrome: Report of a Two-Stage Strategy and Literature Review

Liu

2019

Breast Care

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“…В литературе описаны единичные случаи ис-пользования свободных аутотрансплантатов для реконструкции грудной клетки и молочной желе-зы у больных с синдромом Поланда (нижнеяго-дичный и верхнеягодничный лоскуты, лоскут на основе поверхностной нижней эпигастральной артерии, DIEP-лоскут (перфорантный лоскут на основе нижней эпигастральной артерии), сальник, переднелатеральный лоскут бедра, кожно-мышеч-ный лоскут на основе m. gracilis) [33][34][35][36][37]. Недо-статком данных вмешательств является высокий процент осложнений, «плюсами» -незначитель-ный ущерб для донорской области, а также бы-строе восстановление пациентов по сравнению с транспозицией широчайшей мышцы спины [38].…”

Section: реконструктивные вмешательства на грудной клеткеunclassified

“…Однако, по данным A.E. Seyfer et al (2010), ис-пользование силиконовых имплантатов дает боль-шой процент осложнений [16], и, кроме того, при сложных формах синдрома постановка импланта-та крайне затруднительна [36].…”

Section: реконструктивные вмешательства на грудной клеткеunclassified

Poland’s syndrome

Agranovich

Комолкин

Dimitrieva

2017

Pediatr Traum Orthop Reconstr Surg

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2 ФГБОУ ВО «Санкт-Петербургский государственный педиатрический медицинский университет» Минздрава России, Санкт-Петербург Синдром Поланда -редкий врожденный синдром, характеризующийся частичным или полным односторон-ним отсутствием большой грудной мышцы и врожденным пороком развития кисти со стороны поражения грудной клетки. Также могут быть аномалии ребер (аплазия или гипоплазия) и грудины (килевидная или во-ронкообразная деформация), которые отчетливо пальпируются ввиду истончения подкожно-жирового слоя. Часто при данном синдроме имеются аномалии сосково-ареолярного комплекса. Дефекты грудной клетки обычно носят косметический характер. Мужской пол превалирует над женским в соотношении 2-3 : 1, по ча-стоте преобладает правостороннее поражение. На данный момент общепринятой теорией развития синдрома Поланда является нарушение кровотока по подключичной и/или позвоночной артериям и их ветвям на 6-й не-деле внутриутробного развития. Ввиду полиморфности проявлений синдрома существует множество подходов к объему и срокам оперативной коррекции. В статье мы проанализировали данные по этиопатогенезу и кли-нической картине синдрома Поланда, а также по способам хирургического лечения.Ключевые слова: синдром Поланда, аплазия (гипоплазия) большой грудной мышцы, деформация грудной клетки, брахидактилия, хирургическое лечение. Poland's syndrome is a rare congenital condition classically characterized by partial or complete absence of chest muscles on one side of the body and usually webbing of the fingers of the hand on the same side. There may also be rib (aplasia or hypoplasia) and chest bone abnormalities, which may be noticeable due to less fat under the skin. Breast and nipple abnormalities may also occur, and underarm hair is sometimes sparse or abnormally placed. In most cases, the abnormalities in the chest area do not cause health problems or affect movement. Poland's syndrome most often affects the right side of the body and occurs more frequently in males than in females. The etiology is unknown; however, interruption of the embryonic blood supply to the arteries that lie under the collarbone (subclavian arteries) is the prevailing theory. There are many methods of operative correction because of the polymorphic clinical features of this syndrome. We gathered data on the etiology, pathogenesis, and clinical presentation of Poland's syndrome and reviewed the existing surgical treatment options. POLAND'S SYNDROMEKeywords: Poland's syndrome, aplasia (hypoplasia) of the pectoralis major muscle, chest wall deformity, brachydactyly, surgical treatment. ВведениеСиндром Поланда -врожденный синдром, характеризующийся чаще односторонней (реже двусторонней) гипоплазией (аплазией) большой грудной мышцы (возможно, и малой грудной мышцы) и ребер (как правило, от 2 до 5), ателией

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“…PS [ 7 , 8 ] is a rare congenital anomaly described first in 1897 by Alfred Poland and is characterized by the partial or complete absence of the pectoralis major muscle, ipsilateral symbrachydactyly and is occasionally associated with other malformations of the anterior chest wall and breast.…”

Section: Introductionmentioning

confidence: 99%

Hemidystrophic Thorax Mimicking Scoliosis

Weiss¹,

Seibel²

2018

TOORTHJ

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Background:We regularly use Angle of Trunk Rotation (ATR) measurements for scoliosis screening and also for clinical follow-up of our scoliosis patients under treatment. In some patients, when ATR measurements exceed the screening threshold but without a significant degree of curvature on the X-ray (Cobb angle), a Hemidystrophic Thorax (HDT) is diagnosed. The purpose of this paper was to present a case series of patients with this kind of thoracic deformity because this may be mimicking scoliosis to a significant degree.Materials and Methods:This case series is a consecutive series of patients where the first author detected a hemidystrophic thorax instead of or in combination with scoliosis. A 3D scan of the trunk was made and adjusted to the coordinates in order to achieve an upright orientation of the upper trunk. The scan was scaled in order to determine certain anatomic landmarks, as performed in preparation for bracing. The scan was cut horizontally at the xiphoid level and the plane at this level was analysed visually in order to detect deformations that were different to the typical scoliotic deformations in the horizontal plane.Results:Seven cases were analysed and described in more detail.Conclusion:The condition of HDT may lead to significant rib humps that mimic scoliosis. According to our case series, mild scoliosis can also be associated with HDT. HDT, according to the cases presented in this study, seems to be a relatively benign deformity. Long-term observations are necessary before a final conclusion can be drawn with respect to prognosis.

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Poland's syndrome: A case report with review of literature regarding management

Cited by 9 publications

References 8 publications

Breast Reconstruction with Perforator Flaps in Poland Syndrome: Report of a Two-Stage Strategy and Literature Review

Breast Reconstruction with Perforator Flaps in Poland Syndrome: Report of a Two-Stage Strategy and Literature Review

Poland’s syndrome

Hemidystrophic Thorax Mimicking Scoliosis

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