Pneumonectomy in scimitar syndrome —is it correct?

Karthekeyan, Ranjith Baskar; Yachendra,; Kumar, Siva; Rao, Suresh; Vakamudi, Mahesh; Komarakshi, Balakrishnan; Saldhana, Richard

doi:10.1007/s12055-008-0037-x

Cited by 8 publications

(6 citation statements)

References 5 publications

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“…The rare appearance of a scimitar (Turkish sword) sign on a chest X-ray requires further evaluation including echocardiography verifying the scimitar vein and associated cardiac alterations[ 2 ]; three-dimensional tomography or cardiac magnetic resonance imaging are fundamental for visualizing the anomalous pulmonary vein and clarifying the patient's anatomy. [ 3 ] Cardiac catheterization and angiography can confirm the diagnosis, giving detailed information about the patient's anatomy and the severity of pulmonary hypertension.…”

Section: Discussionmentioning

confidence: 99%

Anesthesia management of living donor liver transplantation in a patient with scimitar syndrome

Muhammad

Majeed²,

Baig³

et al. 2023

Saudi J Anaesth

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Scimitar syndrome is a rare congenital anomaly with a hallmark of an abnormal drainage of pulmonary veins into inferior vena cava instead of the left atrium; this creates a curvilinear radiological pattern resembling a sword (scimitar) on a chest radiograph, thus attracting the name. This case report highlights the challenges during liver transplantation, and perioperative anesthetic management of a patient with an uncorrected Scimitar Syndrome.

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Section: Discussionmentioning

confidence: 99%

Anesthesia management of living donor liver transplantation in a patient with scimitar syndrome

Muhammad

Majeed²,

Baig³

et al. 2023

Saudi J Anaesth

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“…It has greater sensitivity in sever cases of the syndrome and shows associated cardiac alterations 3 . Three-dimensional tomography or cardiac magnetic resonance imaging are fundamental for visualizing the anomalous pulmonary vein and clarifying the patient's anatomy 12 . Cardiac catheterization and angiography confirm the diagnosis, giving detailed information about the patient's anatomy and the severity of the pulmonary hypertension.…”

Section: Discussionmentioning

confidence: 99%

“…Cardiac catheterization and angiography confirm the diagnosis, giving detailed information about the patient's anatomy and the severity of the pulmonary hypertension. They are useful for surgical planning [11][12][13] .…”

Section: Discussionmentioning

confidence: 99%

Scimitar syndrome and anesthetic implications

Luna-Durán

González-Serrano

Echeverry

2015

Colombian Journal of Anesthesiology

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IntubationChild Anesthesia a b s t r a c tWe present a clinical case report of a child with scimitar syndrome and a review of the literature in order to describe the main surgical and anesthetic implications of these patients. Child, 4 months old, weight 4700 g, diagnosed with pneumonia and left lobar emphysema requires mechanical intubation and ICU care. The associated diagnoses are failed extubation, severe pulmonary hypertension and scimitar syndrome confirmed with echocardiography. He was scheduled for pulmonary lobectomy. His mother signed an informed consent authorization for anesthesia and surgery. The child entered surgery, intravenous anesthetic induction was performed and a central venous catheter, an arterial line, urinary catheter and pre-and post-ductal pulse oximeters were inserted. He required vasopressor support with dopamine and transfusion of red blood cells. No adverse events during surgery. At the end of the surgery he was carried back to pediatric ICU and intubated with a chest tube. Extubation was successfully performed 2 days later with favorable progress. Scimitar syndrome is characterized by an anomalous right pulmonary venous return associated with congenital heart disease and pulmonary malformations. It has a low prevalence in the population but a very high perioperative morbidity and mortality, especially in children.With this report we present the main standards and practices for anesthetic management, monitoring and hemodynamic goals with these patients.Cimitarra se caracteriza por un drenaje venoso pulmonar anómalo derecho asociado a cardiopatías congénitas y malformaciones pulmonares. Tiene una prevalencia baja dentro de la población pero una morbimortalidad perioperatoria muy alta sobretodo en niños. Con este reporte se presentan unas pautas concretas y prácticas para el manejo anestésico, la monitorización y las metas hemodinámicas de estos pacientes.

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“…Scimitar syndrome, also known as hypogenetic right lung, venolobar syndrome, Halasz syndrome, mirror image lung syndrome, epibronchial right pulmonary artery syndrome, or vena cava bronchovascular syndrome, is characterized by abnormal pulmonary venous return from a part of or the entire right lung to the inferior vena cava, anomalous arterial supply to the right lung base, and right lung hypoplasia. [ 13 ] This vein presents an oblique caudal course, resembling the short, curved sword called scimitar, and in 15% of cases, it is associated with horseshoe lung. [ 4 6 ]…”

mentioning

confidence: 99%

“…[ 2 ] The two main indications for surgical intervention are large left-to-right shunt >2:1, resulting in pulmonary hypertension or heart failure, and recurrent pulmonary infection associated with sequestered lungs. [ 13 21 22 ]…”

mentioning

confidence: 99%