Pityriasis Rubra Pilaris

Successful use of etanercept in type I pityriasis rubra pilaris

“…PRP usually has no preceding event. However, infection and UV radiation can be provocative 1 . Our patient underwent an urgent appendectomy concurrent with phototherapy.…”

“…PRP has been divided into five categories by Griffiths according to the age at onset, clinical presentation and natural course 1 . Among these, type I – the classical adult form – is the most frequently seen; it usually resolves in approximately 3 years.…”

Treatment of pityriasis rubra pilaris with ustekinumab

“…Its aetiology is unclear. There are six different types of PRP, with a distinction in adult‐onset disease between a typical form and an atypical form with and without human immunodeficiency virus (HIV) infection 1 …”

Pityriasis rubra pilaris type 1 spontaneously resolving after 20 years

“…Many patients with PRP or psoriasis go through phases where one may resemble the other, making clinical diagnosis difficult and leaving the relationship between the two diseases enigmatic. The question as to whether ‘chronic PRP’ could be a slowly evolving prelymphomatous condition was discussed in the 2004 Dowling Oration of PRP 6 . There were no signs of progression in our patient’s clinical, haematological or histological findings.…”