Pituitary sellar spine in a pediatric patient with diabetes insipidus

Sellar spine: A rare Bony variant of the Sella Turcica

“…In all the described cases, the sellar spine was located in the midline in keeping with the foremost theory that it is an ossified remnant of the notochord. 1 , 2 , 3 , 4 , 5 , 6 , 7 , 8 , 9 , 10 , 11 , 12 , 13 , 14 , 15 , 16 The most consistent imaging morphology of the bony spur among the literature was that of a narrow cylindrical bony stalk with a mildly distended tip and a flattened triangular base in continuity with the dorsum sellae. 1 , 2 , 3 , 9 , 11 , 12 , 13 In most cases, the tip had a smooth contour; however, in one of the cases, it was irregular.…”

“…The age at presentation is varied and ranges from 8 to 53 years, with most of the cases reported between the ages of 13 and 29 years. 1 , 2 , 3 , 4 , 5 , 6 , 7 , 8 , 9 , 10 , 11 , 12 , 13 , 14 , 15 , 16 A possible explanation for this distribution is the slow progressive growth of the sellar spine over time, as well as normal progressive enlargement of the pituitary gland. This combination increases the probability of compression of the pituitary gland and thus the development of symptoms.…”

“… 7 The most common presenting complaint among the reviewed literature was headache. 4 , 6 , 7 , 8 , 13 , 15 The other common neurological manifestation was bitemporal hemianopia due to optic chiasm involvement. 8 , 9 , 15 …”

“… 4 , 6 , 7 , 8 , 13 , 15 The other common neurological manifestation was bitemporal hemianopia due to optic chiasm involvement. 8 , 9 , 15 …”

“…Of the endocrine manifestations, there were varying degrees of hypopituitarism, with diabetes insipidus being the most explicable of these findings. 2 , 9 , 15 Few of the cases demonstrated pituitary hyperfunction, including hyperprolactinaemia and Cushing’s syndrome; the pathophysiological mechanism for this is not understood. 3 , 8 , 12 Our case describes the first presentation with puerperal alactogenesis and mild hypoprolactinaemia.…”