“…Other sites known to be involved are the mandible, mediastinum, long bones, uterus, skull, brain, and epididymis [1, 2]. It occurs in infancy and has no sex predilection [2]. It is also known as melanotic ameloblastoma, melanotic progonoma, pigmented neuroectodermal tumor of infancy, ameloblastic odontoma, congenital melanocarcinoma, congenital pigmented epulis, and retinoblastic teratoma [2].…”