Abstract:Arch Argent Pediatr 2016;114(2):e111-e113 / e111Presentación de casos clínicos RESUMEN La piel marmórea telangiectásica congénita (cutis marmorata telangiectatica congenita, CMTC) es una anomalía vascular congénita rara, a menudo benigna, localizada o generalizada, de etiología desconocida. Se caracteriza por piel marmórea persistente, telangiectasia y flebectasia. Podrían presentarse manifestaciones extracutáneas asociadas con la CMTC en el 18,8-70% de los casos. El diagnóstico de este trastorno se basa en lo… Show more
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