Phacoemulsi f ication in the Case of Colobomatous Macrophtalmos with Microcornea Syndrome

Abstract

Purpose: To report phacoemulsification surgery in a case of colobomatous macrophtalmos with microcornea syndrome. Case report: A 72-year-old male presented with complaints of low vision was evaluated. Biomicroscopic examination of anterior segment revealed cataract and microcornea for both eyes and the finding of microcornea was confirmed by Pentecam HR (Oculus). Dilated fundus examination of left eye revealed retinochoroidal and optic nerve coloboma in the lower half and ultrasonography of the right eye showed that retina was attached but the axial length was more than normal. Phacoemulsification and intraocular lens implantation were planned for the patient who was considered to be colobomatous macrophtalmos with microcornea syndrome accompanied by cataract. Ultrasound bio-microscopy (UBM) could not be performed because of the patient's narrow interpalpebral rim and non-cooperation. Uneventful phacoemulsification was applied to the patient under topical anesthesia. However because of advanced zonular dialysis, intraocular lens implantation could not be performed. Conclusion: Colobomatous macrophtalmos with microcornea syndrome which is characterized by microcornea, retinochoroidal coloboma, increased axial length of the globe and myopia is a very rare condition and cataract surgery in these eyes has some difficulties compared to normal eyes.