Persistent Mullerian Duct Syndrome Presenting with Bilateral Intra-Abdominal Gonadal Tumours and Obstructive Uropathy

Asthana, Sonal; Deo, S. V. S.; Shukla, N.K.; Raina, Vinod; Kumar, Lalit

doi:10.1053/clon.2001.9275

Cited by 7 publications

(9 citation statements)

References 12 publications

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“…6 Pre sen ta ti on with go na dal tu mors is ra re. 8 The risk of ma lig nant trans for ma ti on in these go nads is re por ted to be 15% which is si mi lar to the ra te of ma lig nant trans for ma ti on in ot her cryptorc hid tes tes. 1,3,8 A va ri ety of germ cell tumors ha ve be en re por ted in pa ti ents who ha ve PMDS, se mi no ma be ing the most com mon one.…”

Section: Medical Pathologymentioning

confidence: 96%

“…8 The risk of ma lig nant trans for ma ti on in these go nads is re por ted to be 15% which is si mi lar to the ra te of ma lig nant trans for ma ti on in ot her cryptorc hid tes tes. 1,3,8 A va ri ety of germ cell tumors ha ve be en re por ted in pa ti ents who ha ve PMDS, se mi no ma be ing the most com mon one. 1,8,9 Bi la te ral tu mors are ra re; only six bi la te ral germ cell tu mors ha ve be en do cu men ted.…”

Section: Medical Pathologymentioning

confidence: 96%

“…ho od with in gu i nal her ni as con ta i ning Mül le ri an struc tu res (her ni a ute ri in gu i na le), and as so ci a ted cryptorc hi dism. 6,8 Sin ce se con dary sex cha rac teris tics are nor mal, the syndro me is usually discovered in adults du ring her ni op lasty or as sess ment of in fer ti lity. 8 Most of the se pa ti ents are in fer ti le.…”

Section: Medical Pathologymentioning

confidence: 99%

“…6,8 Sin ce se con dary sex cha rac teris tics are nor mal, the syndro me is usually discovered in adults du ring her ni op lasty or as sess ment of in fer ti lity. 8 Most of the se pa ti ents are in fer ti le. 6 Pre sen ta ti on with go na dal tu mors is ra re.…”

Section: Medical Pathologymentioning

confidence: 99%

“…1,3,8 A va ri ety of germ cell tumors ha ve be en re por ted in pa ti ents who ha ve PMDS, se mi no ma be ing the most com mon one. 1,8,9 Bi la te ral tu mors are ra re; only six bi la te ral germ cell tu mors ha ve be en do cu men ted. 9 Ho we ver, we we re not ab le to find any pub lis hed ca se of bi late ral tes ti cu lar ma lig nancy in TTE with PMDS.…”

Section: Medical Pathologyunclassified

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Bilateral Seminoma Arising in Transverse Testicular Ectopia with Persistent Müllerian Duct Syndrome and its Metastasis to Rudimentary Uterus: Case Report

Sarı¹,

Bölükbaşı²,

Kuşku³

et al. 2011

Turkiye Klinikleri J Med Sci

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Section: Medical Pathologymentioning

confidence: 96%

Section: Medical Pathologymentioning

confidence: 96%

Section: Medical Pathologymentioning

confidence: 99%

Section: Medical Pathologymentioning

confidence: 99%

Section: Medical Pathologyunclassified

See 3 more Smart Citations

Bilateral Seminoma Arising in Transverse Testicular Ectopia with Persistent Müllerian Duct Syndrome and its Metastasis to Rudimentary Uterus: Case Report

Sarı¹,

Bölükbaşı²,

Kuşku³

et al. 2011

Turkiye Klinikleri J Med Sci

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Uterus in a male: persistent mullerian duct syndrome. Report of a case with embryological considerations

Gurrera¹,

Vasquez²,

Grasso³

et al. 2002

Pathologica

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We describe a case of persistent mullerian duct syndrome incidentally found in a 79-year-old man. It was characterized by the presence of a uterus-like retroperitoneal mass composed of an ovoidal corpus and rudimental portio with a central lumen. Histologically the mass was leiomyomatous in nature, closely resembling myometrium, while the central lumen was lined by a monolayer of ciliated cuboidal to columnar epithelium similar to embryo-fetal celomatic epithelium. Although this is a dysembryogenetic syndrome due to the lack of regression of the mullerian duct, it may be incidentally discovered in elderly patients, as in the present case during hernioplastic surgery. We also briefly discuss the regression of mullerian duct, focusing on morphological features observed in a large collection of human embryos and fetuses, in order to better understand the pathogenesis of a "uterus' in a male without evidence of sexual abnormalities.

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The Persistent Müllerian Duct Syndrome

Josso

Cate

Picard

2014

Genetic Steroid Disorders

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Persistent Mullerian Duct Syndrome Presenting with Bilateral Intra-Abdominal Gonadal Tumours and Obstructive Uropathy

Cited by 7 publications

References 12 publications

Bilateral Seminoma Arising in Transverse Testicular Ectopia with Persistent Müllerian Duct Syndrome and its Metastasis to Rudimentary Uterus: Case Report

Bilateral Seminoma Arising in Transverse Testicular Ectopia with Persistent Müllerian Duct Syndrome and its Metastasis to Rudimentary Uterus: Case Report

Uterus in a male: persistent mullerian duct syndrome. Report of a case with embryological considerations

The Persistent Müllerian Duct Syndrome

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