Persistent fetal vasculature and spontaneous hyphema in a patient with Klippel-Trénaunay-Weber syndrome

Dhir, Luna; Quinn, Anthony G.

doi:10.1016/j.jaapos.2009.12.157

Cited by 8 publications

(3 citation statements)

References 7 publications

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“…1 We agree that there is no capillary malformation or lymphatic component in our case. This patient had venous malformation on the left lower limb, which was hypertrophied.…”

Section: Replysupporting

confidence: 76%

Persistent fetal vasculature and spontaneous hyphema in a patient with Klippel-Trenaunay-Weber syndrome

Alomari

2010

Journal of American Association for Pediatric Ophthalmology and

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“…1 We agree that there is no capillary malformation or lymphatic component in our case. This patient had venous malformation on the left lower limb, which was hypertrophied.…”

Section: Replysupporting

confidence: 76%

Persistent fetal vasculature and spontaneous hyphema in a patient with Klippel-Trenaunay-Weber syndrome

Alomari

2010

Journal of American Association for Pediatric Ophthalmology and

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“…Ophthalmic features of KT syndrome are orbital varix, retinal varicosities, choroidal angioma, melanoma, persistent fetal vasculature, heterochromia iridum, and glaucoma [4]. Several fundus changes have been reported in the cases of KT and KTW syndromes [5].…”

Section: Discussionmentioning

confidence: 99%

Unilateral Cataract and Vitreoretinopathy in a Case with Klippel-Trenaunay Syndrome

Olcaysu

Altun

Olcaysu

et al. 2014

Case Reports in Ophthalmological Medicine

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Purpose. We present a case with Klippel-Trenaunay (KT) syndrome that had unilateral mature cataract and vitreoretinopathy. Case Report. A 17-year-old boy with KT syndrome presented to the clinic of ophthalmology for low vision in the right eye. His best corrected visual acuity (BCVA) was hand motion in the right eye and 20/20 in the left eye. Anterior segment examination revealed mature cataract in the right. During the physical examination, port-wine stains were noted over right side of his face, ankle, and toes. He had asymmetric face and his head was larger on the right side. Leg lengths were symmetrical, although he had skin hypertrophy. Cranial magnetic resonance imaging studies showed cortical atrophy discordant to his age, asymmetric vascular dilatations in the right hemisphere, hypertrophy in the right periorbital soft tissue, and choroidal plexus. The patient received an uncomplicated cataract surgery. His BCVA in the right eye improved to 20/200 after the surgery. After removing cataractous lens, we were able to examine the fundus that revealed severe vitreoretinopathy and choroidal hemangioma. Conclusion. This case emphasizes the importance of prompt ophthalmic examination in patients with KT syndrome.

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“…1 Ophthalmic features of KTS and KTWS include orbital varix, retinal varicosities, choroidal angioma and melanoma, persistent fetal vasculature, heterochromia iridum, and glaucoma. 3 In addition, various optic nerve anomalies have been described in association with KTSW. Good and Hoyt 4 reported a case of a 10-year-old girl with KTWS and optic nerve shadow enlargement.…”

Section: Discussionmentioning

confidence: 99%

Bilateral optic nerve drusen and gliomas in Klippel-Trenaunay syndrome

Bothun¹,

Kao²,

Guo³

et al. 2011

Journal of American Association for Pediatric Ophthalmology and

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Persistent fetal vasculature and spontaneous hyphema in a patient with Klippel-Trénaunay-Weber syndrome

Cited by 8 publications

References 7 publications

Persistent fetal vasculature and spontaneous hyphema in a patient with Klippel-Trenaunay-Weber syndrome

Persistent fetal vasculature and spontaneous hyphema in a patient with Klippel-Trenaunay-Weber syndrome

Unilateral Cataract and Vitreoretinopathy in a Case with Klippel-Trenaunay Syndrome

Bilateral optic nerve drusen and gliomas in Klippel-Trenaunay syndrome

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