Peripapillary Staphyloma

Abstract

Although extremely rare, the peripapillary staphyloma may cause severe visual impairment of the affected eye in an otherwise healthy individual unassociated with systemic abnormalities.

Congenital disorders of the optic nerve: excavations and hypoplasia

“…41 Two out of six patients with frontonasal dysplasia in association with basal encephalocele were found to have either unilateral or bilateral peripapillary staphyloma. 42 Both facial capillary haemangioma 43 and linear nevus sebaceous syndrome are rare associations.…”

Cystic peripapillary staphyloma: A report of two cases

“…Peripapillary staphylomas of different magnitudes have been described 8,9 ; however, a cystic appearance has only rarely been described. Fernandez-Vigo and colleagues 10 used the term giant peripapillary staphyloma to describe a globe divided into 2 spherical compartments of similar size connected by an opening of 4 mm.…”

Congenital Anomalies of the Optic Nerve

“…Visual acuity is usually low, and compared to other CODA is rarely associated with other congenital defects or systemic diseases. 44 Compared to MGDA, optic disc and vessels are usually normal. Also, a deeper excavation is seen and the glial tuft is absent.…”