Perioperative considerations in Walker–Warburg syndrome

Valk, M. J. A.; Loer, Stephan A.; Schober, Patrick; Dettwiler, S.

doi:10.1002/ccr3.334

Cited by 4 publications

(1 citation statement)

References 18 publications

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“…Rhabdomyolysis and unspecific hypermetabolic responses triggered by volatile anesthetics (e.g., sevoflurane) or succinylcholine have been described in CMD and various myopathies. [ 9 10 ]…”

Section: Discussionmentioning

confidence: 99%

Perioperative total intravenous anesthesia in a child with Walker-Warburg syndrome: A case report

et al. 2022

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Purpose: Walker-Warburg syndrome is a rare autosomal recessive congenital muscular dystrophy presenting with hydrocephalus, type II lissencephaly, cerebellar malformation, and ocular anomalies. Here, we describe the use of perioperative total intravenous anesthesia in a pediatric patient with Walker-Walburg syndrome. Clinical Features: A 2-month-old girl with Walker-Walburg syndrome was admitted for urgent ventriculoperitoneal shunt insertion. Anesthesia was induced using intravenous atropine (100 μg), ketamine (10 mg), and fentanyl (15 μg). The patient was monitored for various clinical parameters based on American Society of Anesthesiologists standards. Anesthesia was maintained using intermittent doses of 0.5 mg intravenous midazolam and 5–10 μg fentanyl in incremental boluses. The postoperative course was uneventful. Conclusions: To our knowledge, no published cases have reported the use of total intravenous anesthesia in patients with Walker-Walburg syndrome who have potential risks for anesthetic-induced malignant hyperthermia. This report described the key features, potential anesthetic management plan, and current literature review of Walker-Walburg syndrome.

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“…Rhabdomyolysis and unspecific hypermetabolic responses triggered by volatile anesthetics (e.g., sevoflurane) or succinylcholine have been described in CMD and various myopathies. [ 9 10 ]…”

Section: Discussionmentioning

confidence: 99%

Perioperative total intravenous anesthesia in a child with Walker-Warburg syndrome: A case report

et al. 2022

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Management of patients susceptible to malignant hyperthermia: A surgeon's perspective

Carlson

Sun

Swan

et al. 2022

International Journal of Pediatric Otorhinolaryngology

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Case Report of Cardiac Arrest After Succinylcholine in a Child With Muscle-Eye-Brain Disease

Hackmann

Skidmore

MacManus³

2017

A & A Case Reports

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Muscle-eye-brain disease is a rare autosomal recessive disorder characterized by congenital muscular dystrophy, ocular abnormalities, and brain malformation. We report an intraoperative hyperkalemic cardiac arrest following the administration of succinylcholine in a child with muscle-eye-brain disease. The disease was diagnosed only after this event. Our experience suggests that preoperative determinations of serum concentrations of lactate and creatine kinase may be useful if clinical signs consistent with myopathy are present.

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Perioperative considerations in Walker–Warburg syndrome

Cited by 4 publications

References 18 publications

Perioperative total intravenous anesthesia in a child with Walker-Warburg syndrome: A case report

Perioperative total intravenous anesthesia in a child with Walker-Warburg syndrome: A case report

Management of patients susceptible to malignant hyperthermia: A surgeon's perspective

Case Report of Cardiac Arrest After Succinylcholine in a Child With Muscle-Eye-Brain Disease

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