Perioperative complications in children with Apert syndrome: a review of 509 anesthetics

Barnett, Sarah S.; Moloney, Claire; Bingham, Robert

doi:10.1111/j.1460-9592.2010.03457.x

Cited by 47 publications

(37 citation statements)

References 14 publications

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“…In an emergency, an intraosseous or intramuscular route can be used. 2 These patients tend to sweat a lot and unlike other patients undergoing syndactyly surgery do not appear to need warming when undergoing peripheral surgery to their limbs. If they are actively warmed there is a risk of pyrexia, so temperature should always be monitored.…”

Section: Discussionmentioning

confidence: 99%

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Anaesthetic Concerns in a Case of Apert Syndrome Posted for Syndactyly Release

Kabade¹,

Lokeshappa²,

Yshya³

et al. 2016

jemds

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Apert syndrome is an autosomal dominant disease presenting with craniosynostosis, midface hypoplasia and syndactyly. Children with Apert syndrome usually present to the operating room for craniofacial and extremity operations. During anaesthesia, difficult intubation and ventilation is expected because of abnormal airways. In case of Apert syndrome, anaesthetists must be prepared for intubation difficulties, airway, ventilation problems and even visceral anomalies. We report a case of Apert syndrome referred to us for endoscopy of upper respiratory tract and syndactyly release. This article will focus on the difficulties and complications related to the anaesthetic management.

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Section: Discussionmentioning

confidence: 99%

“…1 Children with Apert syndrome have a much higher incidence of perioperative airway and respiratory complications than other children. 1,2 We report our experience in the anaesthetic management of a case of Apert syndrome referred to us for endoscopy of upper respiratory tract and syndactyly release procedures.…”

Section: Introductionmentioning

confidence: 99%

Anaesthetic Concerns in a Case of Apert Syndrome Posted for Syndactyly Release

Kabade¹,

Lokeshappa²,

Yshya³

et al. 2016

jemds

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“…Even if intubation was easy, intraoperative respiratory complications are not uncommon. Case studies has reported increase in secretion and wheezing during anesthesia in Apert syndrome (4,(7)(8)(9). Increases in secretion may lead to desaturation and obstruction of tracheal tube (4,7).…”

Section: Discussionmentioning

confidence: 99%

“…Maintenance of airway is a major concern for anesthesiologists in the patients with Apert syndrome (1,4). Ventilation by face mask may be difficult due to craniofacial malformations such as midface hypoplasia, choanal atresia and tracheal stenosis (5).…”

Section: Introductionmentioning

confidence: 99%

Anesthesia for tracheostomy in an infant with Apert syndrome

Acar¹,

Uysal²,

Köseoğlu³

et al. 2013

Gaziantep Med J

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Apert syndrome is a rare, autosomal dominantly inherited disease characterized by irregular craniosynostosis and some malformations involving face, hands and feet. Respiratory functions are frequently deteriorated due to hypoplasia of oropharyngeal and nasopharyngeal cavities. Obstructive sleep apne syndrome, cor pulmonale and sudden death syndrome are among the complications of Apert syndrome. All of these anatomical and physiopathological disorders in the airways lead to a significant concern during anesthesia practice. Difficulty in mask ventilation, difficult intubation and postoperative airway obstruction may be seen in these patients. In this case report we present our anesthetic experience in an infant with Apert syndrome whom anesthesia was given for tracheostomy and difficult intubation was encountered. Keywords: Apert syndrome; infant; general anesthesia Özet Apert sendromu, irregüler kraniosinostoz ile yüz, eller ve ayaklarda malformasyonlarla karakterize otozomal dominant geçişli nadir görülen bir hastalıktır. Orofarengeal ve nazofarengeal kavitelerin hipoplazisi nedeniyle, sıklıkla solunumsal fonksiyonlar bozulur. Obstrüktif uyku apne sendromu, kor pulmonale ve ani ölüm sendromu Apert sendromunun komplikasyonları arasındadır. Havayollarına ait tüm bu anatomik ve fizyopatolojik bozukluklar, anestezi uygulaması sırasında dikkatli olmayı gerektirir. Bu hastalarda maske ventilasyonunda zorluk, zor entübasyon ve postoperatif havayolu obstrüksiyonu görülebilir. Bu olgu sunumunda, trakeostomi nedeniyle anestezi uygulanan ve zor entübasyonla karşılaşılan Apert sendromlu bir bebekteki anestezi deneyimimizi sunuyoruz.

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“…5,6 It is defined by the triad of syndactyly, craniofacial abnormalities, and craniosynostosis. Others conditions include developmental delay, bulging and downward-slanting eyes at the lateral canthus, cleft palate, abnormal occlusion, cervical vertebral fusion, and hydrocephalus.…”

Section: Discussionmentioning

confidence: 99%

Alternative Methods for Nasotracheal Intubation and Extubation in a Patient With Apert Syndrome

Tsukamoto

Yokoyama

2015

Anesthesia Progress

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Apert syndrome is a rare autosomal dominant disorder characterized by craniofacial abnormalities, craniosynostosis and syndactyly. Nasotracheal intubation for a patient with Apert syndrome can be a challenge because of abnormal facial anatomy. We experienced the anesthetic management of a patient with Apert syndrome who underwent partial resection of mandible and cleft palate repair with nasotracheal intubation. Nasotracheal intubation using a gastric tube and extubation using an airway exchange catheter proved useful in this case of airway compromise.

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Perioperative complications in children with Apert syndrome: a review of 509 anesthetics

Cited by 47 publications

References 14 publications

Anaesthetic Concerns in a Case of Apert Syndrome Posted for Syndactyly Release

Anaesthetic Concerns in a Case of Apert Syndrome Posted for Syndactyly Release

Anesthesia for tracheostomy in an infant with Apert syndrome

Alternative Methods for Nasotracheal Intubation and Extubation in a Patient With Apert Syndrome

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