Performance of endoscopic ultrasound for diagnosis of agenesis of the dorsal pancreas: a case report

Abstract

Agenesis of the dorsal pancreas is a rare congenital pancreatic malformation. We herein describe a 67-year-old woman with a 5-day history of lower back pain who was eventually diagnosed with agenesis of the dorsal pancreas. Abdominal computed tomography showed an enlarged pancreatic head, but the pancreatic body and tail were invisible. The magnetic resonance imaging findings were similar to the computed tomography findings. Magnetic resonance cholangiopancreatography showed that the major pancreatic duct was mildly dilated but otherwise normal. Endoscopic ultrasound revealed absence of the pancreatic body and tail, an enlarged head of the pancreas, and mild pancreatic duct dilation. The final diagnosis was dorsal pancreatic agenesis.

Agenesis of the dorsal pancreas with chronic suppurative pancreatitis

“…[ 33 , 34 ] Although the application of endoscopic ultrasound in the diagnosis of ADP has been proved to be effective and reliable. [ 19 ] In the present case, CT scanning and ERCP was firstly performed preoperatively, and surgery finally confirmed the diagnosis of ADP by revealing the absence of the body and tail of the pancreas.…”

“…The clinical features of 17 cases reported in Chinese region were summarized in Table 1. [5][6][7][8][9][10][11][12][13][14][15][16][17][18][19] These cases aged from 15 to 67 and comprised 5 males and 13 females, among whom one case was confirmed the diagnosis by autopsy. [6] The first case of ADP was also incidentally found by autopsy in 1911.…”

“…[1,2] Up to now, around 100 cases of ADP have been reported worldwide since 191, [3,4] whereas <20 cases have been reported in China as we know so far. [5][6][7][8][9][10][11][12][13][14][15][16][17][18][19] Here we reported a a case of ADP with chronic suppurative pancreatitis and evaluated the clinical features of patients with ADP in China.…”

A Rare Case of Dorsal Agenesis of Pancreas, Choledochal Cyst, and Hirschsprung Disease in a Young Patient

“…It has also been shown to demonstrate the dilated proximal pancreatic duct and the absent neck, body, and tail aiding in diagnosis. 12 , 18 …”

“…A few may present with abdominal pain, loss of weight, pancreatitis, diabetes mellitus, exocrine insufficiency, and rarely pancreatic adenocarcinoma in the ventral component of pancreas. 18 – 20 A dorsal agenesis itself does not require any treatment. However, when it is accompanied with an endocrine or exocrine insufficiency, supplementation may be required.…”