Pentalogy of Cantrell - A Case Report from Nigeria

Abstract

The pericardium was absent and the great vessels were exposed. There was an epigastric omphalocoele and a ventral diaphragmatic defect. The diagnosis of Pentallogy of Cantrell was made. The challenges involved in the evaluation and management of this case in a Nigerian setting are discussed.Pentallogy, Cantrell, Nigeria. Keywords:Received Abstract: FB was delivered at home to a para three low income m o t h e r, a t t e r m a f t e r a n unsupervised pregnancy. At birth she was noticed to have an anterior chest wall defect with a protruding p u l s a t i n g m a s s . F u r t h e r examination revealed a defect from the suprasternal notch to the xiphoid process (bifid sternum) with the heart exposed and pulsating (ectopia cordis).

Pentalogy of Cantrell; complete expression in a nine-month-old-boy

“…Pentalogy of Cantrell often have a poor outcome which is dependent on the severity of the malformations 8. Though some cases of pentalogy of Cantrell had been reported in Nigeria, its true prevalence is not known and none of those reported had been proven to completely fulfill the five main components of the pentad 91011. We, therefore, report a case of pentalogy of Cantrell in a 9-month-old boy who completely fulfilled the diagnostic criteria.…”