“…They are slow-growing progressive tumors with an extremely poor prognosis [7,8]. Symptoms are nonspecific (abdominal pain, distention, dyspnea, weight loss, back pain) and may precede the diagnosis by several years [9,10]. However, some tumors may also present with more distinct signs such as an abdominal mass, deep venous thrombosis due to IVC occlusion, or less commonly as an acute Budd-Chiari syndrome [11].…”