PEComa of the Nose: Report of a Case with Immunohistochemical and Ultrustructural Studies and a Review of the Literature

Abstract

PEComas are a family of mesenchymal neoplasms that have in common the presence of a unique cell type,

Rare case of angiomyolipoma of the larynx

“…Not all PECs are epithelioid and some have spindled or adipocyte‐like morphology. Spindled PECs strongly express myogenic markers, whereas epithelioid PECs strongly express HMB‐45 10,11 . In addition, AML occurring in the head and neck region is usually relatively small, in contrast to AML arising in the kidney or liver, which is often large 12 .…”

“…Spindled PECs strongly express myogenic markers, whereas epithelioid PECs strongly express HMB-45. 10,11 In addition, AML occurring in the head and neck region is usually relatively small, in contrast to AML arising in the kidney or liver, which is often large. 12 The CT findings of AML occurring in the head and neck region that have been reported so far are characterized by well delimited and unenhanced.…”

Malignant subcutaneous PEComa on the cheek

“… 1 HMB45 is considered the most sensitive marker for PEComa, followed by Melan-A. 5 Smooth muscle actin (SMA) is the most widely described smooth muscle marker. 1 Meanwhile the desmin marker is more prevalent in cutaneous cases as compared to visceral cases.…”

“… 1 Meanwhile the desmin marker is more prevalent in cutaneous cases as compared to visceral cases. 1 , 5 …”