Partial anomalous pulmonary venous connection to the right side of the heart

Gustafson, Robert A.; Warden, Herbert E.; Murray, Gordon F.; Hill, Ronald C.; Rozar, G.Edward

doi:10.1016/s0022-5223(19)34264-3

Cited by 93 publications

(54 citation statements)

References 29 publications

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“…It is not uncommon, for example, for patients with PAPVR to present with multiple anomalous pulmonary veins and a concomitant sinus venosus ASD. 27,28 In the evolution of our adoption of 4D-PC into our clinical-translational practice, we have seen a gradual transition in our perception and usage of this pulse sequence. We initially adopted 4D-PC as a purely research sequence.…”

Section: Discussionmentioning

confidence: 99%

Improved quantification and mapping of anomalous pulmonary venous flow with four‐dimensional phase‐contrast MRI and interactive streamline rendering

Hsiao

Yousaf

Alley

et al. 2015

Magnetic Resonance Imaging

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Background Cardiac MRI is routinely performed for quantification of shunt flow in patients with anomalous pulmonary veins, but can be technically-challenging to perform. Four-dimensional phase-contrast (4D-PC) MRI has potential to simplify this exam. We sought to determine whether 4D-PC may be a viable clinical alternative to conventional 2D phase-contrast MR imaging. Methods With institutional review board approval and HIPAA-compliance, we retrospectively identified all patients with anomalous pulmonary veins who underwent cardiac MRI at either 1.5 Tesla (T) or 3T with parallel-imaging compressed-sensing (PI-CS) 4D-PC between April, 2011 and October, 2013. A total of 15 exams were included (10 male, 5 female). Algorithms for interactive streamline visualization were developed and integrated into in-house software. Blood flow was measured at the valves, pulmonary arteries and veins, cavae, and any associated shunts. Pulmonary veins were mapped to their receiving atrial chamber with streamlines. The intraobserver, interobserver, internal consistency of flow measurements, and consistency with conventional MRI were then evaluated with Pearson correlation and Bland-Altman analysis. Results Triplicate measurements of blood flow from 4D-PC were highly consistent, particularly at the aortic and pulmonary valves (cv 2–3%). Flow measurements were reproducible by a second observer (ρ = 0.986–0.999). Direct measurements of shunt volume from anomalous veins and intracardiac shunts matched indirect estimates from the outflow valves (ρ = 0.966). Measurements of shunt fraction using 4D-PC using any approach were more consistent with ventricular volumetric displacements than conventional 2D-PC (ρ = 0.972–0.991 versus 0.929). Conclusion Shunt flow may be reliably quantified with 4D-PC MRI, either indirectly or with detailed delineation of flow from multiple shunts. The 4D-PC may be a more accurate alternative to conventional MRI.

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Section: Discussionmentioning

confidence: 99%

Improved quantification and mapping of anomalous pulmonary venous flow with four‐dimensional phase‐contrast MRI and interactive streamline rendering

Hsiao

Yousaf

Alley

et al. 2015

Magnetic Resonance Imaging

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“…An associated cardiac defect, such as an ASD, may either exacerbate or alleviate disease progression. 8 In our patient, the predominant clinical picture was the increased pulmonary blood flow due to ASD and PAPVC. Chest x-ray and ECG were not conclusive.…”

Section: Discussionmentioning

confidence: 60%

Partial Anomalous Pulmonary Venous Connection Associated with Lutembacher's Syndrome

et al. 2008

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Lutembacher's syndrome is a rare combination of congenital atrial septal defect and mitral stenosis (almost always rheumatic). The hemodynamic effect of this combination makes the clinical diagnosis difficult due to a wide variation of clinical presentation. Echocardiography and cardiac catheterization are useful tools for proper diagnosis and planning of the therapeutic strategy. We present a 28-year-old female with Lutembacher's syndrome associated with partial anomalous pulmonary venous connection (PAPVC), which was surgically corrected. To our knowledge, this combination has never been reported in the literature.

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“…At both short-and long-term followup, the Warden procedure has been found to be safe with a low risk of postoperative morbidity, 1,12,25,26 including a low risk of SND. 10,22,[27][28][29] As a consequence, the Warden procedure has been recommended as the surgical technique of choice for repair of SVASD in those patients with high insertion of anomalous pulmonary veins 22 or for all patients with SVASD. 27 We sought to determine whether the Warden procedure resulted in less SND over long-term follow-up when compared with other surgical techniques.…”

Section: Discussionmentioning

confidence: 99%

Long-term Noninvasive Arrhythmia Assessment after Surgical Repair of Sinus Venosus Atrial Septal Defect

Glatz¹,

McBride²,

Paridon³

et al. 2010

Congenital Heart Disease

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Partial anomalous pulmonary venous connection to the right side of the heart

Cited by 93 publications

References 29 publications

Improved quantification and mapping of anomalous pulmonary venous flow with four‐dimensional phase‐contrast MRI and interactive streamline rendering

Improved quantification and mapping of anomalous pulmonary venous flow with four‐dimensional phase‐contrast MRI and interactive streamline rendering

Partial Anomalous Pulmonary Venous Connection Associated with Lutembacher's Syndrome

Long-term Noninvasive Arrhythmia Assessment after Surgical Repair of Sinus Venosus Atrial Septal Defect

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