Parry–Romberg syndrome affecting one half of the body

Abstract

Parry-Romberg syndrome, which is also known as progressive hemifacial atrophy, is a poorly understood rare condition. In this condition, the face shows unilateral, slowly progressive atrophy. Disturbance in fat metabolism, viral infection, trauma, heredity, endocrinal disturbances, and autoimmunity are few possible factors in its pathogenesis. Rarely, only this syndrome progresses and involves one half of the body. Our attempt is to present a case of Parry–Romberg syndrome involving one half of the body, which is a rarity in itself.

Progressive Hemifacial Atrophy and Linear Scleroderma En Coup de Sabre: A Spectrum of the Same Disease?

“…The changes create a sunken hemiface appearance ( 6 , 17 ). As far as it is “hemifacial” the involvement of half of face is usual, but Pathi and colleagues reported a case of involving one-half of the body ( 52 ).…”

Bone Resorption of the Jaws and Occlusal Disturbances in Parry-Romberg Syndrome

“…Parry-Romberg Syndrome is a rare disease that encompasses aesthetics and functionality of the involved tissues. Considered differential diagnosis for Parry-Romberg Syndrome are Rasmussen Syndrome, circumscribed scleroderma and hemifacial dystrophy [6], [7]. It is a self-limiting condition and there is no developed cure for such disease [8].…”