Parry-Romberg syndrome: A case report of non-invasive treatment

Abstract

Parry-Romberg syndrome is an uncommon condition, self-limiting with slow progressive hemifacial atrophy. This syndrome can lead to several progressive congenital and developmental deformities. It can cause severe facial asymmetry and subsequently lead to esthetic and psychological problems and adversely affect patient's quality of life, so its treatment holds great importance. Still, there is no exact treatment protocol for this disease, treatment approaches are bounded and patient's response to the treatment is imponderable. However, most of the patients can benefi t from conservative treatments. In this paper, we have reported a moderate case of Parry-Romberg syndrome, with no familial history of any syndromes. We also have discussed about present anomalies and the steps of exerted conservative treatments.

Disturbances of the stomatognathic system and possibilities of its correction in patients with craniofacial morphea

“…The Inigo classification, based on the degree of atrophy of the bony structures and branches of the trigeminal nerve, divides the PHA syndrome into three categories [16,19,20] (Table 2).…”

“…The inability to close the lips freely increases the likelihood of diseases of the oral mucosa. The inability to close the edges of the lips also impairs the swallowing process [16,[20][21][22][23][24][25][26][27]. Structural deficits in the course of PHA translate into functional impairments in chewing, swallowing, speech and breathing.…”

“…The intercellular interaction, the relationship between cells and the intercellular matrix, and the chemotactic interaction between the neural crest cells and the adjacent plaques guarantee the proper shaping of the facial structures. Due to the extensive role of NCC in the differentiation of facial structures, they are perceived as a presumed causative factor of Parry-Romberg syndrome and other abnormalities associated with facial malformations [14][15][16]. It is said that the inducing factor that initiates the occurrence of the linear form of morphea and PHA may be an injury [1,17].…”

“…The structure of tooth crowns usually does not differ from the norm. On the other hand, there are anomalies within the tooth roots, manifested by their distortion and shortening [16,20,[23][24][25][26][27]. Trigeminal neuralgia manifests itself in the form of acute pain (rarely dull and continuous) lasting from several seconds to several minutes, triggered during chewing, brushing teeth, washing the head [28] (Figure 1).…”

“…However, it should be emphasized that after achieving remission, properly planned therapy in the field of maxillofacial and maxillofacial orthopaedics allows for the correction of the asymmetric pattern of hard tissue growth and thus enables the rehabilitation of the stomatognathic system [16,20,34].…”