Parry-Romberg syndrome: A case report and an insight in to the advances in its pathophysiology and treatment

Karukayil, Deepthi; Sunil, Anuradha; Mukunda, Archana; Basheer, Ashik Bin

doi:10.4103/0976-6944.122960

Cited by 2 publications

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“…Several oral manifestations could be associated with PRS. [ 5 25 26 27 28 29 30 31 32 33 34 35 36 37 ] The oral mucosa and tongue can be affected, also jaws, salivary glands and teeth [ Table 1 ]. There is deviation of the mouth and nose toward the affected side.…”

Section: Systemic and Oral Manifestationsmentioning

confidence: 99%

Oral manifestations of Parry-Romberg syndrome: A review of literature

et al. 2015

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Parry–Romberg syndrome (PRS) or progressive facial hemiatrophy is a developmental craniofacial disorder of unknown etiology characterized by a slowly progressive unilateral facial atrophy. It is associated with different systemic manifestations particularly, maxillofacial, neurologic and ophthalmologic abnormalities. Dentists must be aware of PRS to identify this invalidating disorder. In this article, we review the etiology, clinical features (especially craniofacial and dental manifestations) and treatment of PRS. We searched in PubMed line using specific words such as PRS from 2008 to 2014 (August). We identify 14 papers have described oral manifestations of this syndrome. We excluded all the article papers that did not indicate to oral manifestations of PRS.

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Section: Systemic and Oral Manifestationsmentioning

confidence: 99%

Oral manifestations of Parry-Romberg syndrome: A review of literature

et al. 2015

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“…[13,22] Several oral manifestations could be associated with PRS. [5,25,26,27,28,29,30,31,32,33,34,35,36,37] The oral mucosa and tongue can be affected, also jaws, salivary glands and teeth [Table 1]. There is deviation of the mouth and nose toward the affected side.…”

Section: Systemic and Oral Manifestationsmentioning

confidence: 99%

“…Osseous and dental findings Unilateral tongue atrophy [5,[16][17][18][19][20][21] Jaw hypoplasia [5,17,18,[20][21][22][23][24][25][26][27] Wasting of masticatory muscles [20,21,25] Short roots on affected side [17, 18, 20-22, 24, 27] Deficiency of soft and hard palate [5,21] Delayed ipsilateral tooth eruption [5,19,20,[22][23][24] Unilateral crossbite [5,19,20,[22][23][24]…”

Section: Soft Tissue Changesmentioning

confidence: 99%

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2015

Avicenna J Med

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limb hypoplasia, [7] congenital ipsilateral cerebral atrophy, [8] microphthalmia [9] and renal malformations. [9] Moreover, hypertrophic cardiomyopathy, [10] hypothyroidism, [11] rheumatoid arthritis, [12] lupus erythematosus [9] and scleroderma [13][14][15] are some developmental conditions reported in PRS.Parry-Romberg syndrome, although rare, has been reported in the literature quite abundantly, and has been associated with multiple findings. The treatment options offered in the literature are diverse but not curative. [16] The present review highlights the etiology, clinical oral manifestations and treatment of PRS. ETIOLOGYDespite PRS being recognized for >150 years, the exact etiology and pathogenesis of this condition is not well understood and seems to be heterogeneous. Cerebral disturbance on fat metabolism, local facial trauma, endocrine disturbances, autoimmunity, heredity, hyperactivity or hypoactivity of the sympathetic nervous system, abnormality of the trigeminal nerve and viral infections, including Parry-Romberg syndrome is associated with several developmental and congenital deformities, such as neurologic, ophthalmologic, cardiac, endocrine, autoimmune, cranio-maxillofacial and orthodontic abnormalities. [5] Congenital manifestations that might be associated with PRS are contralateral Poland Syndrome, [6] congenital lower

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Parry-Romberg syndrome: A case report and an insight in to the advances in its pathophysiology and treatment

Cited by 2 publications

References 0 publications

Oral manifestations of Parry-Romberg syndrome: A review of literature

Oral manifestations of Parry-Romberg syndrome: A review of literature

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