“…Although myxoma commonly occurs in skeletal and cardiac muscles (50% of benign cardiac tumors are represented by myxoma, 75% of cases of cardiac myxoma occurs in left atrium, followed by the right atrium (18%), the right and left ventricles (3% in each), and the valves (1%). Multiple myxoma represents 5% of the cases, half of which are of bilateral origin, on the other hand, the recurrence rate of skeletal myxoma is exceptional while in cardiac myxoma is rare and observed in 3% of patient due to inadequate resection or malignant change, and many recurrences are at a different site and multifocal disease occurs frequently in the familial setting), 4 rarely occur in the genitalia like paratesticular region, 2 the genitourinary tract is an unusual location for this tumor; only one case had been reported in the literature which was missed diagnosed for sacro-sciatic hernia and the treatment was unsuccessful by herniorraphy on the contrary of our case in which the diagnosis was in a good time such as the correct treatment. 3 Many cases have been reported in the kidney; whereas, nephrectomy has been reported due to suspicion to malignancy, in the follow up of the patients there had been no sign of malignancy, such as metastasis and recurrence.…”