Palatal myoclonus

Abstract

Palatal miyoklonus, son derece nadir görülen bir hastalıktır. Tinnitus yumuşak damağın ritmik istemsiz hareketlerine bağlı olarak oluşur. Klinik tanı dışarıdan duyulabilen kulakta tıklama sesiyle beraber yumuşak damak hareketlerinin görülmesi ile konur. Bu yazıda, on yıldır kulakta tıklama sesi öyküsü olan ve esansiyel palatal miyoklonus tanısı konulan 38 yaşında bir kadın olgu sunuldu. Hastalık ve semptomatik palatal miyoklonus ile ayırıcı tanısı literatür verileri ışığında değerlendirildi.Anahtar Sözcükler: Esansiyel palatal miyoklonus; objektif tinnitus; semptomatik palatal miyoklonus.Palatal myoclonus is an extremely rare disorder. Tinnitus is secondary to rhythmic involuntary movements of the soft palate. Clinical diagnosis is based on the confirmation of the soft palate movements synchronous with an audible clicking noise outside. In this article, we report a 38-year-old female case with a 10 yearhistory of continuing ear click, who was diagnosed with essential palatal myoclonus. The disease and its differential diagnosis from symptomatic palatal myoclonus were discussed in the light of literature data.

Wernekink commissure syndrome with palatal myoclonus at onset: a case report and review of the literature

“…In contrast to the cases previously reported in the literature (Table 1 ) with palatal myoclonus occurring several months after ischemic stroke, our patient presented with palatal myoclonus from the onset. Matsuo et al and Tuna et al ., in their case reports, hypothesized that delayed palatal myoclonus was secondary to lesions involving the Guillain-Mollaret triangle leading to delayed transsynaptic degeneration of bilateral inferior olivary nuclei [ 7 , 14 , 15 ]. The onset of palatal myoclonus with acute stroke in our patient questions this hypothesis because there was no evidence of left inferior olivary nucleus degeneration seen on imaging (Fig.…”