1983
DOI: 10.1016/0002-8703(83)90253-3
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Osler-Weber-Rendu disease with multiple intrahepatic arteriovenous fistulas

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Cited by 34 publications
(9 citation statements)
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“…The incidence of liver involvement in HHT is unknown, but it appears the lesion is uncommon, with fewer than 80 cases reported in the literature. 7,9,11,[13][14][15][20][21][22][23][24][25][26][27][28][29] From the literature, the most common indication for therapeutic intervention for symptomatic hepatic involvement is highoutput cardiac failure. Conversely, mesenteric angina was the indication for treatment of hepatic AVMs in a single case in the literature.…”
Section: Discussionmentioning
confidence: 99%
See 1 more Smart Citation
“…The incidence of liver involvement in HHT is unknown, but it appears the lesion is uncommon, with fewer than 80 cases reported in the literature. 7,9,11,[13][14][15][20][21][22][23][24][25][26][27][28][29] From the literature, the most common indication for therapeutic intervention for symptomatic hepatic involvement is highoutput cardiac failure. Conversely, mesenteric angina was the indication for treatment of hepatic AVMs in a single case in the literature.…”
Section: Discussionmentioning
confidence: 99%
“…1 Hepatic involvement in HHT is probably less common but has been reported. 1,[8][9][10][11][12][13][14] The hepatic vascular malformations of HHT, like those of the central nervous system, can be of several different forms, including large AV fistulas, telangiectasias, and hepatic artery (HA) aneurysms, occasionally in the context of cirrhosis. 8,12 Nineteen cases of hepatic telangiectasias associated with fibrosis and/or cirrhosis were collected by Martini.…”
mentioning
confidence: 99%
“…Over 50 cases of HHT presenting as hepatic arteriovenous fistulae and/or telangiectasia have been reported [55][56][57], although the true incidence may be much higher. Chronic liver disease is present in up to 30% of patients with HHT [30].…”
Section: Hepatic Manifestationsmentioning
confidence: 99%
“…Portosystemic encephalopathy should be managed in the standard fashion. Portal hypertension can be controlled by propranolol, but in severe cases might require embolization or surgical ligation of the shunt [56,69,70]. Variceal bleeding is managed in the standard fashion acutely but may require hepatic artery embolization or ligation for long-term control [62].…”
Section: Hepatic Manifestationsmentioning
confidence: 99%
“…Immunosuppressive therapy was Discussion M. Osler is an autosomal dominant disorder [lo] characterized by the classical triad of mucocutaneous and visceral teleangiectasia, recurrent epistaxis, and a positive family history. Liver involvement with typical arteriovenous fistulas and teleangiectasias has been reported in more than 50 cases [5,101. In a few cases, these pathological features were also associated with fibrosis and cirrhosis [8].…”
Section: Case Reportmentioning
confidence: 99%