Anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA) is a rare entity. Brooks described
first cases in 1885. Only 25% to 30% % of cases are associated with congenital defects such as aortopulmonary
window and tetralogy of Fallot. It is recommended the reimplantation of the right coronary artery in the Aorta, with
redistribution of coronary flow avoiding the signs of ischemia or other complications even when the diagnosis is done
in asymptomatic patients. This is the report of two infants with who debuted with murmur and signs of heart failure.
ARCAPA and Pulmonary Aortic Window were diagnosed and they were surgically corrected through intrapulmonary
tunneling with a favorable evolution.