Operative Korrektur einer Sklerodermie en coup de sabre durch En-bloc-Resektion

Abstract

A 15-year-old patient developed scleroderma en coup de sabre on right temple at 5 years of age. Multiple treatments (3 cycles of intravenous penicillin, topical glucocorticosteroids, topical calcipotriol, and cream PUVA phototherapy combined with topical calcipotriol) produced no improvement. The patient suffered greatly from the psychosocial stigmatization, so that the entire lesion was resected at 14 years of age. One year after the operation a thin non-sclerotic scar was present; tiny lateral areas of sclerosis not included in the operative field were unchanged. The operation greatly improved the patient's daily life. The surgical therapy of scleroderma en coup de sabre offers an interesting therapeutic alternative.

Therapeutic and Reconstructive Management Options in Scleroderma (Morphea) en Coup de Sabre in Children and Adults. A Systematic Literature Review

“…Surgical removal of the band-shaped sclerosis is possible as an alternative therapy of localized scleroderma en coup de sabre. There was one case of a patient with localized scleroderma en coup de sabre who was successfully treated with an en bloc resection of the band-shaped sclerotic area [42].…”