Occipital Encephalocele Associated With a Dermoid Cyst

Martínez‐Lage, Juan F.; Poza, Máximo; Ramos, José Francisco Dória; Almagro, María-José; Sempere, Manuel; Mestre, J. Dios Berná

doi:10.1177/088307389200700419

Cited by 9 publications

(8 citation statements)

References 9 publications

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“…The majority of congenital encephaloceles occur in the occipital or frontal regions [1,2]. Dermoid cyst with frontal encephalocele is not uncommon, but only one case of occipital encephalocele with dermoid cyst has been reported [3,4,5,6]. We report a case of infratorcular occipital meningoencephalocele with dermoid cyst.…”

Section: Introductionmentioning

confidence: 91%

“…They are associated with midline craniofacial dysraphism. Sphenoidal encephaloceles are often clinically occult and usually become apparent at the end of the first decade of life [3,4,5,6]. Because skull ossification begins at 10 weeks’ gestation, diagnosis is usually not possible before this time.…”

Section: Discussionmentioning

confidence: 99%

“…We report the present case believing that the dermoid and the encephalocele might be pathogenetically related although at present no data statistically support this idea. The occurrence of a dermoid cyst with frontal encephalocele is not uncommon, but only one case of occipital encephalocele with a dermoid cyst has been reported [6]. …”

Section: Discussionmentioning

confidence: 99%

“…The quantity and location of protruding neural tissue determine the neurologic deficits. Visual defects, psychomotor developmental delay, and persistent motor deficits frequently occur [2,6,10,12]. …”

Section: Discussionmentioning

confidence: 99%

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Infratorcular Meningoencephalocele with Dermoid Cyst

Mahore¹,

Fonseca²,

Dange³

et al. 2010

Pediatr Neurosurg

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Section: Introductionmentioning

confidence: 91%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

See 2 more Smart Citations

Infratorcular Meningoencephalocele with Dermoid Cyst

Mahore¹,

Fonseca²,

Dange³

et al. 2010

Pediatr Neurosurg

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show abstract

“…Among the cases presented here, only one had dismorhic features but also had normal karyotype, and her findings did not match the above syndromes. In the presence of an encephalocele, there is a 60-80% risk of associated structural abnormalities like optical, choroidal and retinal dysplasia, [16], severe ocular alterations [17], central nervous system anomalies [18], dermoid cyst [19], tectocerebellar dysraphia [20], and necrosis [21]. More than 60% of these patients may also develop hydrocephalus requiring a V-P shunt [22,23].…”

Section: Journal Of Neurology and Neuroscience Issn 2171-6625mentioning

confidence: 99%

New born children with Encephalocele

Uğraş¹,

Kavak²

2016

J Neurol Neurosci

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The child with a cephalocele: etiology, neuroimaging, and outcome

et al. 1996

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We report a series of 46 children who were treated for one of the diverse forms of cranium bifidum during a period of 22 years. The purpose of the survey was to investigate pathogenetic factors involved in the development of cranial dysraphism and to analyze clinical and pathological factors that influence the patients' outcome. We also investigated the existence of associated intracranial anomalies, in a systematic way, using modern methods of neuroimaging, and related the findings to the patients' final results. The lesions were classified as encephalocele (n = 15), cranial meningocele (n = 3), atretic cephalocele (n = 26), cranium bifidum occultum (n = 1), and exencephaly (n = 1). There was an excess of the atretic form of cephaloceles in our series, a fact that probably reflects geographical variations described for cephaloceles in general. The location of the lesions was occipital in 29 children, parietal in 16, and temporal and frontobasal in one case each. In seven cases there was parental consanguinity. A familial history of malformations of the central nervous system was encountered in eight instances. Associated systemic abnormalities were present in 23 patients, while central nervous system anomalies were found in 36 children. Cephalocele repair was undertaken on 35 occasions. There were no surgical fatalities in the series. The mean follow-up time was of 7 years. Overall mortality for the whole group was of 17/46 or 36%. Twenty of the 29 survivors had no neurological sequelae, but only 18 children exhibited a competitive intelligence level. A good outcome was found to correlate well with: an average head size at birth, a normal initial neurological condition, operability of the lesions, and an absence of disorders of the neuronal migration. Neurological outcome depended also on the occurrence or not of hydrocephalus, while the intelligence level was mainly related to the absence of cerebral tissue within the sac of the malformation.

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Occipital Encephalocele Associated With a Dermoid Cyst

Abstract: The case of a neonate with a dermoid cyst originating within an occipital encephalocele is reported. The finding of the tumor was made during the routine repair of the meningoencephalocele. To our knowledge this is the first time that this association has been described.

Cited by 9 publications

References 9 publications

Infratorcular Meningoencephalocele with Dermoid Cyst

Infratorcular Meningoencephalocele with Dermoid Cyst

New born children with Encephalocele

The child with a cephalocele: etiology, neuroimaging, and outcome

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