Spontaneous or non-traumatic cerebrospinal fluid leaks comprise 5%-10% of all cerebrospinal fluid (CSF) rhinorrhea [1,2]. Generally, CSF rhinorrhea can occur at the cribriform plate, sella, sphenoid sinus, or ethmoid air cells [3,4]. However, primary CSF rhinorrhea due to clival defect is extremely rare. The current study describes two cases of spontaneous CSF rhinorrhea through the clivus which were repaired with endoscopic endonasal transsphenoidal approach. Such cases are extremely rare and upon literature review, only 16 cases with clival defect are reported thus far. The peculiar aspect of this case report is related to its rarity.