Non classical Potter’s sequence: a rare complication of chronic oligohydramnios

Abstract

Chronic oligohydramnios due to any cause can have grave foetal prognosis. One of the rare complications is Potter's sequence which occurs as a result of intrauterine mechanical compression of the foetus due to decreased liquor volume. This case report aims to give an insight into this rare complication. Classical Potter's sequence is due to renal cause whereas non classical, a still rarer variant of Potter's sequence is due to non renal cause. We describe a case of a lady at 38 weeks of gestational age with chronic oligohydramnios due to prolonged leaking per vaginum and severe intrauterine growth restriction. She delivered a congenitally malformed male baby with features of Potter's sequence. The renal abnormalities were conspicuously absent in our case, suggesting a diagnosis of non classical Potter sequence.

A Typical Case of Classic Potter’s Syndrome: A Case Report

“…Potter syndrome is a rare clinical syndrome first described by Edith Potter in 1946 at the Chicago Hospital in the USA. Characterized by facial features in infants with bilateral renal agenesis and oligohydramnios [1]. Its incidence varies from 1 in 2000 to 5000, with an average of 1 in 4000, reported in 0.2% -0.4% of autopsies of newborns who died immediately after birth.…”

Rare manifestations of Potter Sequence: A Case Report

“…Potter sequence was first described by Edith Potter 1946 at the Chicago Lying Hospital in the U.S.A that consisted of facial characteristics in infants with bilateral renal agenesis. 1 The sequence with an incidence of 1 in every 2,000 to 5,000 fetuses is associated with a recurrence risk of 3-6% and is found in 0.2-0.4% of autopsies in dead new-borns or those who die immediately after birth. 2 It includes clubbed feet, pulmonary hypoplasia and cranial anomalies related to oligohydramnios.…”