Neurological sequelae of the dancing eye syndrome

Pohl, Keith; Pritchard, Jon; Wilson, John

doi:10.1007/bf01953945

Cited by 59 publications

(57 citation statements)

References 38 publications

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“…No child with disease of equal severity exhibits spontaneous improvement. 19,20 Others have reported poor outcomes for moderate and severe OMS, 21,22 and the relapse rate with conventional treatment is 68%. 20 Our patient has experienced no relapses.…”

Section: Discussionmentioning

confidence: 99%

Immunologic and Clinical Responses to Rituximab in a Child With Opsoclonus-Myoclonus Syndrome

et al. 2005

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Section: Discussionmentioning

confidence: 99%

Immunologic and Clinical Responses to Rituximab in a Child With Opsoclonus-Myoclonus Syndrome

et al. 2005

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“…In Pohl et al's cohort of 54 patients with DES from all causes a 'persisting disability was found in 88%'. 3 They comment that the 'neurological legacy of DES is often evident well into childhood'. 3 Mitchell et al reviewed records of 17 children with DES who had had neuroblastomas resected and found 'cognitive development and adaptive behaviour were delayed or abnormal in nearly all'.…”

Section: Discussionmentioning

confidence: 99%

“…3 They comment that the 'neurological legacy of DES is often evident well into childhood'. 3 Mitchell et al reviewed records of 17 children with DES who had had neuroblastomas resected and found 'cognitive development and adaptive behaviour were delayed or abnormal in nearly all'. 4 The infant in this case report was monitored in the orthoptic department for several years following resection of the neuroblastoma.…”

Section: Discussionmentioning

confidence: 99%

Dancing eye syndrome: a case presentation

Parker¹,

Edwards

2012

British and Irish Orthoptic Journal

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Aim: To describe a case of a 14-month-old girl who presented to the eye clinic with unusual bouts of horizontal nystagmoid movements. Methods: The orthoptic findings are presented, along with the investigation results, underlying pathology, treatment and long-term prognosis. Results: A thoracic neuroblastoma was identified on chest X-ray and subsequent CT scan. After resection of the tumour the initial presenting sign of intermittent opsoclonus persisted. Conclusions: This case shows the presentation of an infant with dancing eye syndrome (DES), secondary to a thoracic neuroblastoma. Following the surgical resection of the primary tumour the intermittent opsoclonus remained. The ocular motility slowly returned to normal but some neurological sequelae persisted.

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“…Em 40 a 80%dos casos, pode-se detectar um neuroblastoma oculto (2,6,9,10) , constituindo uma síndrome paraneoplásica. Raramente evidenciam-se em adultos outros tipos de neoplasias, como linfoma não Hodgkin, adenocarcinoma renal e melanoma, entre outros (5,11) . A SK também pode se associar ao pós-operatório de transplante de células tronco hematopoiéticas (12) .…”

Section: Discussionunclassified

Síndrome de Kinsbourne manifestando-se com quadro de encefalite pós-viral

Andrade

Troster

Cypel

2011

Rev. paul. pediatr.

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OBJETIVO: Descrever um caso de síndrome de Kinsbourne manifestando-se com quadro de encefalite pós-viral e rever a da literatura. DESCRIÇÃO DO CASO: Criança do sexo feminino, dois anos e seis meses, encaminhada de outro serviço com história de ataxia, irritabilidade e dificuldades articulatórias na fala após episódio prodrômico de febre, lesões de pele e mucosa. Com hipótese de encefalite pós-viral, a avaliação clínica evidenciou quadro de síndrome opsoclônus-mioclonia-ataxia ou síndrome de Kinsbourne. Foi afastada a associação de neuroblastoma oculto e iniciada terapêutica com corticosteroide. Durante internação e acompanhamento ambulatorial, houve regressão progressiva e normalização do quadro clínico e neurológico inicial. COMENTÁRIOS: Apesar de se tratar de uma doença rara, o diagnóstico de síndrome de Kinsbourne deve ser reconhecido pelos pediatras e intensivistas, com objetivo de instituir tratamento específico precoce, embora com resultados variáveis, sendo fundamental a exclusão de neuroblastoma oculto.

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Neurological sequelae of the dancing eye syndrome

Abstract: Demonstrable malignancy is uncommon in the dancing eye syndrome. The neurological legacy of DES is often evident well into adult life.

Cited by 59 publications

References 38 publications

Immunologic and Clinical Responses to Rituximab in a Child With Opsoclonus-Myoclonus Syndrome

Immunologic and Clinical Responses to Rituximab in a Child With Opsoclonus-Myoclonus Syndrome

Dancing eye syndrome: a case presentation

Síndrome de Kinsbourne manifestando-se com quadro de encefalite pós-viral

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