Neurenteric cysts—A spectrum

Al-Rabeeah, Abdullah A.; Gillis, Delores; Giacomantonio, Michael; H, Lau

doi:10.1016/s0022-3468(88)80418-4

Cited by 84 publications

(42 citation statements)

References 14 publications

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“…More subtle anomalies, such as spina bifida occulta, may be indicated only by the presence of hypertrichosis, a nevus, angioma, or a sacral dimple. Associated anomalies are diverse, and those present in our case as mentioned by others [6,8,9,[11][12][13][14][15][16][17][18][19][20][21][22] are listed in Table 1. Bentley and Smith stated that malformations of the heart and the great vessels have also been associated with abnormal spinal development, but a ready explanation is not at hand [6].…”

Section: Discussionmentioning

confidence: 86%

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A case of split notochord syndrome: a child with a neuroenteric fistula presenting with meningitis

Ramshorst

Lequin

Mancini

et al. 2006

Journal of Pediatric Surgery

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The authors describe a case of split notochord syndrome with a neuroenteric fistula in a newborn presenting with meningitis. Associated anomalies included agenesis of the corpus callosum, short colon, malrotation, epispadias, and an abnormally high bifurcation of the abdominal aorta and inferior vena cava. The embryological mechanisms and etiologic theories are discussed in short. D 2006 Elsevier Inc. All rights reserved.Split notochord syndrome (SNS) describes congenital spinal anomalies, associated with anomalies of the vertebrae, central nervous system, and gastrointestinal tract. The anomalies arise from a persistent connection between endoderm and dorsal ectoderm. Depending on its size, site, and point in time, abnormal splitting of the notochord can result in a wide variety of malformations and clinical symptomatology. Case reportA 4-day-old boy was referred to our hospital on suspicion of meningitis with secondary dehydration and for evaluation of vertebral anomalies. He was born at 37 weeks of gestation through normal vaginal delivery as the third child of a 26-year-old mother. Birth weight was 3010 g. Physical examination revealed normal tonus, minor facial dysmorphic signs (eg, broad mouth and dysmorphic, normally placed ears with a thin helix), left-sided congenital hip dysplasia, sacral dimple, and rocker bottom feet. The penis showed a mild epispadias, whereas anus, scrotum, and testes were normal. The mother had smoked during pregnancy and had not used supplementary folic acid. Besides local treatment of a vaginal yeast infection, no other medication had been used during pregnancy. The day before, the patient had been brought in at the referring hospital with a 2-day history of poor feeding and fever. He was jaundiced and showed a tachycardia at a body temperature of 398C. Neurologic examination revealed high tonus and a bulging anterior fontanel. The abdomen was distended. Abdominal x-ray showed a spinal cleft of the vertebrae of Th 12 and L1 (Fig. 1). The kidneys were normal on ultrasound. Blood tests showed elevated C-reactive protein (109 mg/L) and white blood cell count (25,500 cells per cubic millimeter). No lumbar puncture was attempted because of the vertebral anomalies. Blood cultures showed growth of Escherichia coli bacteria, after which, antibiotic treatment was switched from amoxicillin/ cefotaxim to meropenem.

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Section: Discussionmentioning

confidence: 86%

“…Complicated anomalies may be easy to detect, even antenatally [7]. Clinical presentation of SNS may include gastrointestinal obstruction or meningitis [8][9][10]. More subtle anomalies, such as spina bifida occulta, may be indicated only by the presence of hypertrichosis, a nevus, angioma, or a sacral dimple.…”

Section: Discussionmentioning

confidence: 99%

A case of split notochord syndrome: a child with a neuroenteric fistula presenting with meningitis

Ramshorst

Lequin

Mancini

et al. 2006

Journal of Pediatric Surgery

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“…Very few number of posterior mediastinal enteric cysts have been reported in the neonatal period and early childhood (8)(9)(10). It is difficult to differentiate cyst type preoperatively.…”

Section: Discussionmentioning

confidence: 99%

Yenidoğan döneminde nadir bir solunum sıkıntısı nedeni: posterior mediyastinal gastroenterik kist

Taşkın¹,

Özcan²,

Satar³

et al. 2011

tpa

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A A r ra ar re e c ca au us se e o of f r re es sp pi ir ra at to or ry y d di is st tr re es ss s i in n t th he e n ne eo on na at ta al l p pe er ri io od d: : p po os st te er ri io or r m me ed di ia as st ti in na al l g ga as st tr ro oe en nt te er ri ic c c cy ys st t E Er rd da al l T Ta afl flk k› ›n n, , K Ke en na an n Ö Öz zc ca an n* *, , M Me eh hm me et t S Sa at ta ar r* *, , N Ne ej ja at t N Na ar rl l› ›* *, , F Fe er rd da a Ö Öz zl lü ü* *, , H Ha ac ce er r Y Ya ap p› ›c c› ›o o¤ ¤l lu u* * IntroductionThe patient was born at term by cesarean section as the fourth living baby from the seventh pregnancy of a preeclamptic mother of 35 years old and a healthy father of 43 years old who had no consanguinity. Apgar score was found to be 5 in the first minute and 8 in the fifth minute. The male baby who had a prediagosis of cystic adenoid malformation in the left lung on ultrasonographical examination performed in the 34 th gestational week prenatally was hospitalized in the Neonatal Intensive Care Unit after birth. Physical examination findings were as follows: birth weight 3400 g (50-75% p), head circumference 35 cm (50-75% p), heigth 49 cm (50-75% p), pulse rate 152/min, blood pressure 78/32 mmHg. Slight prolongation of expirium in the left lung areas compared to the rigth lung areas was found on lung oscultation. Heart sounds were normal, peripheral pulses were palpated simultaneously with heart sounds. No organomegaly was found on abdominal examination and orogastric catheter was inserted into the stomach. Baseline arterial blood gases were as follows: pH: 7.35, PaCO 2 : 43 mmHg, PaO2:71 mmHg, HCO3: 19 mmol/l and oxygen saturation: 95%. Complete blood count and serum biochemical values including sodium, potassium, urea, creatinine, calcium and blood glucose were within normal limits. Right and left paracardial consolidated mass with regular contours was found on thorax graphy and corpus defect was noted in T3, T4 and T5 vertebrae (Picture 1). On thoracic computarized tomography, a large mass lesion pushing the trachea, esophagus and aorta mainly in the right side starting from the upper part of the diaphragm and extending to the upper part of tracheal bifurcation was observed. The cyst was found to be consisted of two parts (Picture 2). On esophagography, 1/3 lower part of the esophagus was dislocated anteriorly and slightly to the left and was compressing the trachea. On echocardiographic examination a cystic formation with dimensions of 3.5x5 cm was found behind the heart adjacent to the left atrium. The patient who had no problem until the 4 th day of life developed respiratory distress on the 4 th day. Blood gases measured simultaneously were as fol- C Ca as se e R Re ep po or rt t S Su um mm ma ar ry yPresentation of mediastinal enteric cysts is observed rarely during neonatal period. They are mostly asymptomatic. The commonest mode of presentation in neonatal period is respiratory distress. Basically, diagnosis of enteric cyst is made with histologic findings. In this article, a cas...

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“…Split notochord syndrome can occur at any level in the spine, but the majority of reported cases have involved the cervical or thoracic region (Alrabeeah et al 1988). The cases involving the lumbar region are very rare.…”

Section: Discussionmentioning

confidence: 99%

Split Notochord Syndrome: Ileal Duplication Causing Intermittent Episodes of Vomiting

Tsuchida

Takahashi

Noguchi

et al. 2006

Tohoku J. Exp. Med.

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Neurenteric cysts—A spectrum

Cited by 84 publications

References 14 publications

A case of split notochord syndrome: a child with a neuroenteric fistula presenting with meningitis

A case of split notochord syndrome: a child with a neuroenteric fistula presenting with meningitis

Yenidoğan döneminde nadir bir solunum sıkıntısı nedeni: posterior mediyastinal gastroenterik kist

Split Notochord Syndrome: Ileal Duplication Causing Intermittent Episodes of Vomiting

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