Musculoskeletal case of the day. Gorham syndrome of the right clavicle and scapula.

Glass-Royal, M; Stull, Margaret A.

doi:10.2214/ajr.154.6.2110757

Cited by 10 publications

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“…Gorham-Stout disease has been classified into five groups. (10)(11)(12). Although the previous X-ray did not reveal any abnormality, the patients havesevere pain and the osteolytic process increased rapidly before the fracture.…”

Section: Discussionmentioning

confidence: 92%

Two cases of Gorham-Stout disease with good response to zoledronic acid treatment

Brance¹,

Castiglioni

Cóccaro

et al. 2017

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SummaryGorham-Stout disease -also called vanishing bone syndrome -is a rare bone disease characterized by a progressive intra-osseous proliferation of non-neoplastic vascular tissue resulting in massive osteolysis. Here, we report two clinical cases of Gorham-Stout disease. Case 1: a 56-year-old woman with 20 years of history of pain and swell in elbows, ankles and wrist. Then she was diagnosed as systemic lupus erythematosus (SLE) with glomerulonephritis type III. After other pathologies were ruled out Gorham-Stout disease was diagnosed. Intravenous zoledronic acid (5 mg) was indicated and after third infusion a progressive improvement of pain, mobility and daily activities were observed. Case 2: a 70-years-old man with a history of pain and limited motion in the left shoulder without X-ray abnormality. Six months later pathological fracture in the left humerus occurred and after ruled out other pathologies Gorham-Stout disease was diagnosed. Intravenous zoledronic acid (5 mg) was indicated and a good response was observed after the first infusion. Nowadays just over 200 cases were reported. Gorham-Stout disease was reported in different bones, at different age presentation and severe physical deformities, disabilities, and life-threatening complications can occur. Two cases of Gorham-Stout disease with good response to zoledronic acid was reported in this article.

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Section: Discussionmentioning

confidence: 92%

Two cases of Gorham-Stout disease with good response to zoledronic acid treatment

Brance¹,

Castiglioni

Cóccaro

et al. 2017

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“…The disease occurs within a large spectrum of bones, such as the scapula [19], [20], clavicle [21], [22], ribs [22], [23], femur [24], [25], and maxillofacial bones [9], [26], but the majority of case reports refer to the shoulder and pelvis [16], [27], [28], [29]. GSD can occur in males and females, with a slight predominance in males [30], and has been reported in patients aged 1 [31] to 75 [32] years.…”

Section: Discussionmentioning

confidence: 99%

From tooth extraction to Gorham-Stout disease: A case report

Bocchialini

Ferrari

Burlini

2017

International Journal of Surgery Case Reports

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HighlightsGorham-Stout disease (GSD) is a very rare idiopathic bone disorder characterised by spontaneous and progressive osteolysis, associated with angiomatous proliferation and soft tissue swelling without new bone formation.The clinical presentation of GSD includes pain, functional impairment, and swelling, although a few asymptomatic cases have been reported, similar to our case.We present this rare case of GSD with several localisations to emphasise that any procedure appearing to be simple can go catastrophically wrong and can result in the discovery of something that is unexpected and extremely rare.We wish to emphasise the extreme rarity of the case, focusing on the large difference between the preoperative panoramic radiograph and whole-body CT and MRI images obtained on the day after the first surgical procedure.

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“…The great majority of these cases describe single bone involvement; however, the spread of disease to adjacent bones has been reported, especially in the upper and lower extremities [2, 8–11]. There have been six case reports of spread from the scapula to the clavicle [1, 10, 12, 13], four reports of spread across the glenohumeral joint from the scapula to the proximal humerus [2, 8], and three cases of involvement of both the forearm and carpal bones [2, 11]. Only one previous case of involvement of the radius and ulna with spread to the distal humerus has been reported [9].…”

Section: Introductionmentioning

confidence: 99%

A Rare Case Report of Extensive Polyostotic Gorham's Disappearing Bone Disease Involving the Upper Extremity

Ahlmann

Tunru-Dinh

2011

Case Reports in Orthopedics

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Gorham's disease is a rare disorder involving the proliferation of endothelial channels resulting in resorption and disappearance of bone. An unusual case of polyostotic Gorham's disease affecting the scapula, humerus, radius, and ulna in a 39-year-old woman is described. The patient had extensive disease spreading across both the glenohumeral and humeroulnar joints. This is the first report of Gorham's disease spreading across multiple joints in the upper extremity.

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Musculoskeletal case of the day. Gorham syndrome of the right clavicle and scapula.

Cited by 10 publications

References 0 publications

Two cases of Gorham-Stout disease with good response to zoledronic acid treatment

Two cases of Gorham-Stout disease with good response to zoledronic acid treatment

From tooth extraction to Gorham-Stout disease: A case report

A Rare Case Report of Extensive Polyostotic Gorham's Disappearing Bone Disease Involving the Upper Extremity

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