Multiple-stage correction of caudal duplication syndrome: a case report

Liu, Hao; Che, Xiangming; Wang, Shufeng; Chen, Gang

doi:10.1016/j.jpedsurg.2009.09.018

Cited by 15 publications

(9 citation statements)

References 10 publications

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“…The patient also had hydronephrotic left kidney and left megaureter, which were removed. Ultimate outcome is good [6].…”

Section: Discussionmentioning

confidence: 97%

“…Treatment consists of staged correction of duplication anomalies [6]. Either stripping of mucosa or resection of duplicated colon and rectum is undertaken.…”

Section: Discussionmentioning

confidence: 99%

“…No corrective surgery was, however, done in the adult female patient reported by them. Liu et al [6] reported the case of caudal duplication syndrome in which they did multiple stage correction. The bladder septum was removed, the two hemi-phalluses were fused to form one phallus, and the duplicated colon was excised.…”

Section: Discussionmentioning

confidence: 99%

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Caudal Duplication Syndrome—Report of a Case and Review of Literature

et al. 2013

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A 3-day-old male neonate presented with features of anorectal malformation and duplication of the external genitalia. He was subsequently diagnosed with complete duplication of the colon, rectum, bladder, and urethra associated with spinal lipoma. We report this case of caudal duplication syndrome, considering its rarity and the diverse combination of gastrointestinal, genitourinary, spinal, and limb anomalies.

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“…The patient also had hydronephrotic left kidney and left megaureter, which were removed. Ultimate outcome is good [6].…”

Section: Discussionmentioning

confidence: 97%

“…Treatment consists of staged correction of duplication anomalies [6]. Either stripping of mucosa or resection of duplicated colon and rectum is undertaken.…”

Section: Discussionmentioning

confidence: 99%

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Caudal Duplication Syndrome—Report of a Case and Review of Literature

et al. 2013

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“…The purpose of surgical reconstruction is to have a single anal opening located within the complex muscle either by removal of the anal side opening outside of the sphincter [7,8] or joining of the two anorectal ends and positioning in the muscle sphincter [9]. Depending on the duplication length and anatomical variant, if the two duplicated colons are not fused and have a separate blood supply, one side should be removed if not, stripping of the mucosa on the non-dominant side [10] or stapling the common wall [9] (similar with stapling the common wall in Duhamel procedure [11]) to ensure efficient emptying, to avoid complications such as severe constipation [12] with fecal impaction, volvulus, or neoplastic changes. End-to-side anastomosis of the two colonic lumens should not be the first option because of the risk of stenosis at the anastomotic site in the long-term with fecal impaction and proximal colitis [3].…”

Section: Management Of Colorectal Duplicationmentioning

confidence: 99%

“…In cases with a history of multiple abdominal surgeries and depending on the complexity of procedures, the cesarean surgery should be assisted by a colorectal surgeon and/or urologist. Male patients present with complete or partial penile duplication and are more likely to be corrected for cosmetic reasons with removal of one of the abnormal shafts [13] or penoplasty [12]. There are no reports assessing fertility and sexual function into adult age in CDS male patients.…”

Section: Management Of Genital Duplicationmentioning

confidence: 99%

Caudal Duplication Syndrome Systematic Review—A Need for Better Multidisciplinary Surgical Approach and Follow-Up

et al. 2020

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Background and Objectives: Caudal duplication syndrome is a rare association of anatomical anomalies describing duplication of the hindgut, spine, and uro-genital structures, leading to varied clinical presentations. The current literature focuses on case reports which describe the embryological etiology and anatomical spectrum of the condition giving little attention to the surgical preparation, the need for a well-structured follow-up program, or the transition into adult healthcare of these complex patients. No reviews have been published regarding this complex pathology. Materials and Methods: A review of caudal duplication syndrome cases was done to assess the range of the clinical malformations, timing, and types of surgical interventions. Inconsistencies in multidisciplinary care, follow-up, and risk events were described. Results: Hindgut duplication always involved the anorectal region. Anorectal malformations were evenly distributed as unilateral and bilateral. Colon duplication extended from the anal region to the transverse colon or ascending colon in most of the cases and less to terminal. In females, genital duplication was present in all cases. The follow-up period varied between 3 months and 12 years. In all adult females, the motive of presentation was related to pregnancy (complications after successful delivery, fertility evaluation) or late complications (fecalith obstruction of the end-to-side colon anastomosis, repeated UTIs with renal scarring). Conclusions: Complex malformations affecting multiple caudal organs may have a strong impact in many aspects of the long-term quality of life; therefore, patients with caudal duplication syndrome need increased awareness and joined multidisciplinary treatment.

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