Multiple Phlebectasia Involving Jejunum, Oral Cavity, and Scrotum

Problems of alimentary bleeding.

“…Both patients were without evidence of portal hypertension and had been subject to recurring mild episodes of melaena. Phlebectasia of the small intestine has been described involving the jejunum, with lesions also involving the scrotum (Fordyce lesion) and the oral cavity, with "caviare" spots under the tongue due to clusters of small varicose veins, in patients who have episodes of alimentary bleeding (Rappaport and Shiffman, 1963 ;Miller and Akers, 1968). Bandler (1960) described a 41-year-old patient with numerous episodes of melaena who was found to have venous varicosities of the entire small intestine and who had mucocutaneous pigmentation similar to that described in the Peutz-Jeghers syndrome.…”

Punctate vascular papules on the tongue and scrotum

“…[3] Oral mucosal angiokeratomas have also been associated, uncommonly, with angiokeratomas of the scrotum, gastrointestinal mucosa (jejunum), or both. [4] Recently Ranjan & Mahajan have proposed a clinical classification for oral angiokeratomas, depending on the number of lesions, associated other muco-cutaneous involvement and systemic disease. [3]…”

Bleeding jejunal phlebectasia in an adolescent: case report

“…There are only 18 reported cases in the English literature, and this is the first case within the pediatric population [3][4][5][6][7]. The most frequent mode of clinical presentation is with melena or hematemesis, which can be life threatening [3].…”

“…Jejunal phlebectasias have been described as a type of cavernous hemangioma [5]. However, hemangiomas and other neoplastic vascular lesions consist of a proliferation of abnormal vascular structures that are frequently cavernous, whereas a phlebectasia is a single venous dilatation.…”