Multiple Cutaneous Angiomyxomas in a Child

Abstract

Cutaneous myxomas are rare, benign, connective tissue tumors composed of stellate cells set in a loose mucoid stroma containing delicate reticulin fibers running in various directions. They are also called angiomyxomas to reinforce their vascular component. These lesions have been recognized as part of Carney complex. We report an 11-year-old boy affected by disseminated cutaneous angiomyxomas since the age of 2, without any other component of Carney complex.

Myxoid Nodule on the Leg of an Immunosuppressed Man: A Quiz

“…Histologically, SAs are mainly dermal lesions with frequent extension to the subcutis. SAs are composed of spindle-shaped to stellate cells in a myxoid stroma with a predominantly vascular component ( 7 ). Vimentin is usually positive, CD34 can be positive in SA.…”