Mucous Membrane Pemphigoid Presenting With Esophageal Manifestations: A Case Series

DeGrazia, Taryn; Eisenstadt, Rachel; Willingham, Field F.; Feldman, Ron J.

doi:10.14309/ajg.0000000000000393

Cited by 2 publications

(3 citation statements)

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“…CP is a rare systemic autoimmune blistering disorder that most commonly occurs in middle-aged women. 3 , 4 It produces a blistering rash with inflammatory lesions on mucous membranes that typically cicatrize, leading to irreversible damage. 3 The annual incidence of CP is 1/100,000.…”

Section: Discussionmentioning

confidence: 99%

“… 3 The frequency of esophageal involvement is 2%–30%, and is more likely to be present in disseminated disease, 5 although it was recently reported that esophageal mucous membrane pemphigoid can rarely occur in isolation. 4 CP is a potentially life- and vision-threatening disease because it can lead to asphyxiation and blindness. 3 Early diagnosis and management is imperative to avoid complications.…”

Section: Discussionmentioning

confidence: 99%

“…A high index of suspicion and effective collaboration between gastroenterology and dermatology departments are crucial to achieving optimal treatment results. 4 …”

Section: Discussionmentioning

confidence: 99%

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Esophageal Cicatricial Pemphigoid

Udemba,

Burkholder,

Raja

et al. 2024

ACG Case Rep J

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Cicatricial pemphigoid (CP) is a rare autoimmune blistering disorder, which affects the skin, eyes, and mucous membranes. The annual incidence of CP is 1/100,000. Esophageal involvement is rare and usually occurs in disseminated disease. Esophageal disease presents with dysphagia and weight loss and can be difficult to treat. We present a case of a 65-year-old woman with esophageal CP whose symptoms improved with esophageal dilatation and rituximab infusions.

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Section: Discussionmentioning

confidence: 99%