Mri findings in giant pontine capillary telangiectasis asso - ciated with a developmental venous anomaly

Abstract

We report a 32-year-old woman with an exceptionally large capillary telangiectasia in the brainstem which is associated with a developmental venous anomaly (DVA). Her major problems were nystagmus in both eyes, binocular diplopia, gait abnormalities, cerebellar ataxia, slightly disturbed finger-nose test, an instable Romberg test and obvious dysartria. The diagnosis was made on the basis of specific imaging findings, and the use of gradient echo-weighted images proved to be helpful in making a differential diagnostic decision. Key-word: Telangiectasia.From:

Anomalía del desarrollo venoso asociado a telangiectasia capilar un hallazgo infrecuente: reporte de 2 casos

“…Actual nomenclature for this malformations are based on the histological descriptions performed by Russell and Rubinstein, describing four types: arteriovenous malformations (AVM), cavernous angiomas (CA), capillary telangiectasia (CT) and venous angioma also known as venous development anomalies (VDA) 1,2 , clinically, radiologically and pathologically this lesions are presented as different entities, nevertheless the coexistence of two or more lesions in the same patient have been described in previous publications, binging the possibility that this malformations are the spectrum of an only disease with a unique pathogenesis 1,4 . The most frequent and known association ins cerebral vascular malformations is between cavernous angiomas and venous angiomas, nevertheless the coexistence between venous angiomas and capillary telangiectasia is less frequent, it has been described only in six times according to the literature [5][6][7][8][9][10] , which has captured our attention in order to report the two cases received at a hospital in Bogotá, Colombia, that are described in this paper.…”

Capillary telangiectasia of the brain: imaging with various MR techniques

“…Lately susceptibility weighted imaging (SWI) is being used in the diagnosis, since it has been shown to be more sensitive to susceptibility effects (2, 8-10). Diffusion weighted imaging (DWI) has also been used for the diagnosis of BCTs (1, 11,12).…”